idiopathic interstitial pneumonias


Summary: A group of interstitial lung diseases with no known etiology. There are several entities with varying patterns of inflammation and fibrosis. They are classified by their distinct clinical-radiological-pathological features and prognosis. They include IDIOPATHIC PULMONARY FIBROSIS; CRYPTOGENIC ORGANIZING PNEUMONIA; and others.

Top Publications

  1. Horimasu Y, Ishikawa N, Taniwaki M, Yamaguchi K, Hamai K, Iwamoto H, et al. Gene expression profiling of idiopathic interstitial pneumonias (IIPs): identification of potential diagnostic markers and therapeutic targets. BMC Med Genet. 2017;18:88 pubmed publisher
    ..Moreover, DSG3 is a novel potential biomarker for chronic fibrosing IIP with its significantly high expression in IIP lung. ..
  2. Wallaert B, Monge E, Le Rouzic O, Wemeau Stervinou L, Salleron J, Grosbois J. Physical activity in daily life of patients with fibrotic idiopathic interstitial pneumonia. Chest. 2013;144:1652-1658 pubmed publisher
    ..Quantitation of DLPA is a novel patient-centered approach to assess function in f-IIP and may be a useful tool for clinical care and assessing response to therapy. ..
  3. Adegunsoye A, Oldham J, Valenzi E, Lee C, Witt L, Chen L, et al. Interstitial Pneumonia With Autoimmune Features: Value of Histopathology. Arch Pathol Lab Med. 2017;141:960-969 pubmed publisher
  4. Sato Y, Tanino Y, Wang X, Nikaido T, Sato S, Misa K, et al. Baseline serum syndecan-4 predicts prognosis after the onset of acute exacerbation of idiopathic interstitial pneumonia. PLoS ONE. 2017;12:e0176789 pubmed publisher
    ..Baseline serum syndecan-4 is a possible prognostic biomarker after the onset of acute exacerbation of idiopathic interstitial pneumonia. ..
  5. Travis W, Costabel U, Hansell D, King T, Lynch D, Nicholson A, et al. An official American Thoracic Society/European Respiratory Society statement: Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med. 2013;188:733-48 pubmed publisher
    In 2002 the American Thoracic Society/European Respiratory Society (ATS/ERS) classification of idiopathic interstitial pneumonias (IIPs) defined seven specific entities, and provided standardized terminology and diagnostic criteria...