mitochondrial trifunctional protein


Summary: A mitochondrial protein consisting of four alpha-subunits and four beta-subunits. It contains enoyl-CoA hydratase, long-chain-3-hydroxyacyl-CoA dehydrogenase, and acetyl-CoA C-acyltransferase activities and plays an important role in the metabolism of long chain FATTY ACIDS.

Top Publications

  1. Mozrzymas R, Konikowska K, Regulska Ilow B. Energy exchangers with LCT as a precision method for diet control in LCHADD. Adv Clin Exp Med. 2017;26:515-525 pubmed publisher
    ..This method can be used by doctors and dietitians who specialize in treating rare metabolic diseases. It can also be used by patients and their families for accurate menu planning with limited LCT content. ..