Raffaella A Morotti
Affiliation: Mount Sinai School of Medicine
- Progressive familial intrahepatic cholestasis (PFIC) type 1, 2, and 3: a review of the liver pathology findingsRaffaella A Morotti
The Lillian and Henry Stratton Hans Popper Department of Pathology, Mount Sinai School of Medicine, New York, New York 10029, USA
Semin Liver Dis 31:3-10. 2011..This review focuses mainly on the liver histology, summarizing their characteristic pathologic features, the correlation to specific genotypes, and complications arising with disease progression...
- Pediatric inflammatory myofibroblastic tumor with late metastasis to the lung: case report and review of the literatureRaffaella A Morotti
Department of Pathology, Box 1194, Mount Sinai Medical Center, One Gustave L Levy Place, New York, NY 10029, USA
Pediatr Dev Pathol 8:224-9. 2005..We describe the clinical and pathologic features of this patient and review the characteristics of extrapulmonary IMTs with distant metastasis reported in the literature...
- The changing face of post-transplant lymphoproliferative disease in the era of molecular EBV monitoringNanda Kerkar
Department of Surgery, Mount Sinai School of Medicine, Recanati Miller Transplant Institute, New York, NY 10029, USA
Pediatr Transplant 14:504-11. 2010....
- Chronic rejection preceded by central perivenulitis, rapidly ensuing after liver transplantation in a pediatric patientTamir Miloh
Department of Pediatrics, Mount Sinai School of Medicine, New York, New York, USA
Semin Liver Dis 29:134-8. 2009....
- Multiple exudative ulcers and pseudopolyps in allergic eosinophilic gastroenteritis that responded to dietary therapyMirna Chehade
Department of Pediatric Gastroenterology, Mount Sinai School of Medicine, New York, NY 10029, USA
J Pediatr Gastroenterol Nutr 45:354-7. 2007
- Bullous pemphigoid after liver transplantation for liver failureNanda Kerkar
Division of Pediatric Hepatology, Department of Pediatrics, Mount Sinai School of Medicine, New York, NY, USA
Liver Transpl 12:1705-10. 2006..This child is unique in that his liver function and hemolytic anemia appeared to normalize after liver transplant, but neutropenia and BP both thought to be autoimmune in etiology, developed more than a year post-transplant...
- Hepatitis C in children: a quaternary referral center perspectiveCarolina Rumbo
Department of Pediatrics, Mount Sinai School of Medicine, New York, NY 10029, USA
J Pediatr Gastroenterol Nutr 43:209-16. 2006..3% of children in the United States, and the general impression is that it has a benign course in childhood. We analyzed a pediatric population with chronic HCV in a quaternary referral center...
- Hepatic involvement in congenital acute megakaryoblastic leukemia: a case report with emphasis on the liver pathology findingsMichael S Lewis
Department of Pathology, Mount Sinai School of Medicine, New York, NY, USA
Pediatr Dev Pathol 11:55-8. 2008..Awareness of this unusual clinical presentation and of the characteristic liver pathology may facilitate the pathologic diagnosis...
- Resolution of hepatopulmonary syndrome after auxiliary partial orthotopic liver transplantation in Abernethy malformation. A case reportSukru Emre
Department of Pediatrics, Mount Sinai Medical Center, Mount Sinai School of Medicine, New York, NY, USA
Liver Transpl 13:1662-8. 2007..APOLT is a feasible and successful surgical procedure for patients with Abernethy malformation and HPS...
- Esophageal subepithelial fibrosis in children with eosinophilic esophagitisMirna Chehade
Department of Pediatric Gastroenterology and Nutrition, Mount Sinai School of Medicine, New York, NY 10029, USA
J Pediatr Gastroenterol Nutr 45:319-28. 2007..Our goal was to determine the prevalence of esophageal fibrosis in children with EE, to determine whether it is specific for EE, and to correlate it with clinical and pathological features...
- Farber's disease type IV presenting with cholestasis and neonatal liver failure: report of two casesAsha Willis
Department of Pediatrics and Pediatric Hepatology, Mount Sinai School of Medicine, New York, NY 10029, USA
Pediatr Dev Pathol 11:305-8. 2008..We describe 2 siblings who presented with jaundice in the neonatal period and discuss the clinical data and variation in pathologic findings that should be considered for the diagnosis...
- Hepatocellular carcinoma and congenital absence of the portal vein in a child receiving growth hormone therapy for turner syndromeRaffaella A Morotti
Lillian and Henry M Stratton Hans Popper Department of Pathology, Mount Sinai School of Medicine, New York, New York 10029, USA
Semin Liver Dis 27:427-31. 2007....
- Cystic fibrosis in an adolescent being evaluated for primary sclerosing cholangitisJyoti Sinha
Department of Pediatrics, Mount Sinai School of Medicine, New York, New York 10029, USA
Semin Liver Dis 26:80-4. 2006
- Delayed homicides due to infant head injury initially reported as natural (cerebral palsy) deathsJames R Gill
New York City Office of Chief Medical Examiner, 520 First Avenue, New York, NY 10016, USA
Pediatr Dev Pathol 11:39-45. 2008..All 5 deaths were certified as homicides...
- An immunohistochemical algorithm to facilitate diagnosis and subtyping of rhabdomyosarcoma: the Children's Oncology Group experienceRaffaella A Morotti
Department of Pathology, Mount Sinai School of Medicine, New York, USA
Am J Surg Pathol 30:962-8. 2006..Their differential expression in reactive myogenic lesions, variability in ARMS versus ERMS, and absence in undifferentiated sarcomas suggest new biologic questions to be explored in future studies...
- Renal benign epithelial nodal inclusionsTatiana V Yakoushina
Department of Pathology, Mount Sinai Medical Center, New York, NY 10029, USA
Ann Diagn Pathol 12:181-6. 2008..We report 2 cases of benign renal tubular epithelial inclusions located in the perinephric hilar lymph nodes. One of our cases is, to our knowledge, the first case of benign renal epithelial inclusions reported in an adult patient...
- Rapamycin successfully treats post-transplant autoimmune hepatitisNanda Kerkar
Recanati Miller Transplant Institute, Department of Pediatrics, Division of Pediatric Hepatology, The Mount Sinai School of Medicine, New York, NY, USA
Am J Transplant 5:1085-9. 2005..All six responded to treatment but drug was withdrawn in one patient. Adverse events were minimal. Rapa may prove to be an important addition in the control of autoimmune liver disease...
- Rapid evolution of congenital hepatic fibrosis after liver transplantation for acute liver failure: the potential role of extrahepatic factorsJudith Flores
Department of Gastroenterology, Hospital de Pediatria, Centro Medico Nacional Siglo XXI, Instituto Mexicano del Seguro Social, Mexico City, Mexico
Liver Transpl 14:660-4. 2008..Examination of the explanted liver revealed remarkable progression of the congenital hepatic fibrosis, suggesting that the phenotype of this disease may be dependent in part on extrahepatic factors...
- Risk assignment in pediatric soft-tissue sarcomas: an evolving molecular classificationStephen J Qualman
Division of Anatomic Pathology, Department of Laboratory Medicine, Children s Hospital, 700 Children s Drive, Columbus, OH 43205, USA
Curr Oncol Rep 4:123-30. 2002..Large clinical cooperative trials involving biologic studies of pediatric soft-tissue sarcomas could facilitate advancement of knowledge in this area of pediatric oncology...