Paula H B Bolton-Maggs

Summary

Affiliation: University of Liverpool
Country: UK

Publications

  1. ncbi The management of factor XI deficiency
    P H Bolton-Maggs
    Department of Haematology, Alder Hey Children s Hospital, Liverpool, UK
    Haemophilia 4:683-8. 1998
  2. ncbi Idiopathic thrombocytopenic purpura
    P H Bolton-Maggs
    Royal Liverpool Children s Hospital, Alder Hey, Eaton Road, Liverpool L12 2AP, UK
    Arch Dis Child 83:220-2. 2000
  3. ncbi The nontreatment of childhood ITP (or "the art of medicine consists of amusing the patient until nature cures the disease")
    P H Bolton-Maggs
    Royal Liverpool Children s Hospital, Alder Hey, UK
    Semin Thromb Hemost 27:269-75. 2001
  4. ncbi Haemophilias A and B
    Paula H B Bolton-Maggs
    Department of Haematology, Royal Liverpool Children s Hospital, Liverpool, UK
    Lancet 361:1801-9. 2003
  5. ncbi A review of inherited platelet disorders with guidelines for their management on behalf of the UKHCDO
    Paula H B Bolton-Maggs
    Department of Haematology, Manchester Royal Infirmary, Manchester, UK
    Br J Haematol 135:603-33. 2006
  6. ncbi The prevalence of the cysteine1584 variant of von Willebrand factor is increased in type 1 von Willebrand disease: co-segregation with increased susceptibility to ADAMTS13 proteolysis but not clinical phenotype
    Derrick J Bowen
    Department of Haematology, University of Wales College of Medicine, Cardiff GF14 4XN, UK
    Br J Haematol 128:830-6. 2005
  7. ncbi An investigation of the von Willebrand factor genotype in UK patients diagnosed to have type 1 von Willebrand disease
    Anthony Cumming
    University Department of Haematology, Manchester Royal Infirmary, Manchester, UK
    Thromb Haemost 96:630-41. 2006
  8. ncbi Optimal haemophilia care versus the reality
    Paula H B Bolton-Maggs
    Manchester Haemophilia Comprehensive Care Centre, Manchester Royal Infirmary, Manchester, UK
    Br J Haematol 132:671-82. 2006
  9. ncbi Haemophilia--paucity of evidence, ways forward?
    Paula H B Bolton-Maggs
    Manchester Haemophilia Comprehensive Care Centre, Department of Clinical Haematology, Manchester Royal Infirmary, Manchester, UK
    Blood Coagul Fibrinolysis 14:S7-9. 2003
  10. ncbi Congenital afibrinogenemia: identification and expression of a missense mutation in FGB impairing fibrinogen secretion
    Dung Vu
    Centre Medical Universitaire, 1 rue Michel Servet, CH 1211 Geneva, Switzerland
    Blood 102:4413-5. 2003

Collaborators

Detail Information

Publications11

  1. ncbi The management of factor XI deficiency
    P H Bolton-Maggs
    Department of Haematology, Alder Hey Children s Hospital, Liverpool, UK
    Haemophilia 4:683-8. 1998
    ..If fresh frozen plasma is to be used, it is preferable to obtain one of the virally inactivated products. Fibrin glue is a useful treatment which deserves further study...
  2. ncbi Idiopathic thrombocytopenic purpura
    P H Bolton-Maggs
    Royal Liverpool Children s Hospital, Alder Hey, Eaton Road, Liverpool L12 2AP, UK
    Arch Dis Child 83:220-2. 2000
    ..This is more likely in older children, especially girls. The disease is reviewed with reference to diagnosis, investigation, and management options...
  3. ncbi The nontreatment of childhood ITP (or "the art of medicine consists of amusing the patient until nature cures the disease")
    P H Bolton-Maggs
    Royal Liverpool Children s Hospital, Alder Hey, UK
    Semin Thromb Hemost 27:269-75. 2001
    ....
  4. ncbi Haemophilias A and B
    Paula H B Bolton-Maggs
    Department of Haematology, Royal Liverpool Children s Hospital, Liverpool, UK
    Lancet 361:1801-9. 2003
    ..The future holds the realistic possibility of gene therapy. However, we must not forget that haemophilia is a worldwide disorder that requires significant economic resources not available for the majority...
  5. ncbi A review of inherited platelet disorders with guidelines for their management on behalf of the UKHCDO
    Paula H B Bolton-Maggs
    Department of Haematology, Manchester Royal Infirmary, Manchester, UK
    Br J Haematol 135:603-33. 2006
    ....
  6. ncbi The prevalence of the cysteine1584 variant of von Willebrand factor is increased in type 1 von Willebrand disease: co-segregation with increased susceptibility to ADAMTS13 proteolysis but not clinical phenotype
    Derrick J Bowen
    Department of Haematology, University of Wales College of Medicine, Cardiff GF14 4XN, UK
    Br J Haematol 128:830-6. 2005
    ..Increased susceptibility of C1584 VWF to ADAMTS13 proteolysis may be physiologically significant and increase an individual's risk of bleeding and presenting with VWD...
  7. ncbi An investigation of the von Willebrand factor genotype in UK patients diagnosed to have type 1 von Willebrand disease
    Anthony Cumming
    University Department of Haematology, Manchester Royal Infirmary, Manchester, UK
    Thromb Haemost 96:630-41. 2006
    ..Unless linkage of VWD phenotype with the VWF gene can be clearly demonstrated, the results of any genetic family studies should be interpreted with caution...
  8. ncbi Optimal haemophilia care versus the reality
    Paula H B Bolton-Maggs
    Manchester Haemophilia Comprehensive Care Centre, Manchester Royal Infirmary, Manchester, UK
    Br J Haematol 132:671-82. 2006
    ..The development of inhibitory antibodies seriously complicates the management both in morbidity and cost. While gene therapy has not yet produced the hoped-for cure, new technologies will produce improved products...
  9. ncbi Haemophilia--paucity of evidence, ways forward?
    Paula H B Bolton-Maggs
    Manchester Haemophilia Comprehensive Care Centre, Department of Clinical Haematology, Manchester Royal Infirmary, Manchester, UK
    Blood Coagul Fibrinolysis 14:S7-9. 2003
    ..Some preliminary questions can establish areas where new clinical studies are needed...
  10. ncbi Congenital afibrinogenemia: identification and expression of a missense mutation in FGB impairing fibrinogen secretion
    Dung Vu
    Centre Medical Universitaire, 1 rue Michel Servet, CH 1211 Geneva, Switzerland
    Blood 102:4413-5. 2003
    ....
  11. ncbi The importance of tissue factor source in the management of Factor VII deficiency
    Paula H B Bolton-Maggs
    Manchester Haemophilia, Comprehensive Care Centre, Department of Clinical Haematology, Manchester Royal Infirmary, Manchester, UK
    Thromb Haemost 97:151-2. 2007