Research Topics
| John H J WokkeSummaryAffiliation: University Medical Center Utrecht Country: The Netherlands Publications
| Collaborators
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Detail Information
Publications
Quantification of SMN protein in leucocytes from spinal muscular atrophy patients: effects of treatment with valproic acidSanne Piepers
Rudolf Magnus Institute of Neuroscience, Department of Neurology, University Medical Centre Utrecht, The Netherlands
J Neurol Neurosurg Psychiatry 82:850-2. 2011..Increasing SMN protein production by histone deacetylase inhibiting drugs such as valproic acid (VPA) is an experimental treatment strategy for SMA...
Fatigue is part of the burden of neuromuscular diseasesJohn H J Wokke
J Neurol 254:948-9. 2007
Weighted gene co-expression network analysis of the peripheral blood from Amyotrophic Lateral Sclerosis patientsChristiaan G J Saris
Department of Neurology, Rudolf Magnus Institute of Neuroscience, University Medical Center Utrecht, Utrecht 3584 CX, The Netherlands
BMC Genomics 10:405. 2009..Since access to spinal cord tissue is not possible at disease onset, we investigated changes in gene expression profiles in whole blood of ALS patients...
Clinical features of late-onset Pompe disease: a prospective cohort studyJohn H J Wokke
Universitair Medisch Centrum Utrecht HP G03 228, Heidelberglaan 100, 3584 CX Utrecht, Netherlands
Muscle Nerve 38:1236-45. 2008..The outcome measures were demonstrated to be safe and reliable. Symptom duration was identified as the best predictor of the extent of skeletal and respiratory muscle weakness...
Effect of non-invasive ventilation on survival, quality of life, respiratory function and cognition: a review of the literatureSanne Piepers
Department of Neurology, Rudolph Magnus Institute of Neuroscience, University Medical Centre Utrecht, Utrecht, The Netherlands
Amyotroph Lateral Scler 7:195-200. 2006..All studies suggest a beneficial effect on QoL and other outcome measures (Evidence level Class II-III). Well-designed randomized controlled trials comparing the effect on QoL and survival have not been performed...
Magnesium treatment for patients with refractory status epilepticus due to POLG1-mutationsNora A Visser
Rudolf Magnus Institute of Neuroscience, Department of Neurology, University Medical Centre Utrecht, PO Box 85500, 3508 GA, Utrecht, The Netherlands
J Neurol 258:218-22. 2011..Given the difficulties encountered while treating epilepsy in patients with this syndrome, magnesium therapy might be considered...
Is cold paresis related to axonal depolarization?Hessel Franssen
Department of Neurology, Neuromuscular Disease Group, Rudolf Magnus Institute for Neuroscience, University Medical Center Utrecht, The Netherlands
J Peripher Nerv Syst 15:227-37. 2010..The induced weakness may be explained not only by this mechanism but also by impaired muscle contraction...
Severity of Guillain-Barré syndrome is associated with Fc gamma Receptor III polymorphismsNina M van Sorge
Department of Neurology G03 228, University Medical Center Utrecht, Heidelberglaan 100, 3584 CX Utrecht, The Netherlands
J Neuroimmunol 162:157-64. 2005..Results suggest that Fc gammaRIII genotypes may represent mild disease-modifying factors in GBS...
