Research Topics
| Peter C G NijssenSummaryAffiliation: St. Elisabeth Hospital Country: The Netherlands Publications
| Collaborators |
Detail Information
Publications
Autosomal dominant adult neuronal ceroid lipofuscinosis: parkinsonism due to both striatal and nigral dysfunctionPeter C G Nijssen
Department of Neurology, St Elisabeth Hospital, Tilburg, The Netherlands
Mov Disord 17:482-7. 2002..We conclude that parkinsonism in ANCL is likely to be caused by both presynaptic nigral cell loss and postsynaptic striatal degeneration...
Autosomal dominant adult neuronal ceroid lipofuscinosis: a novel form of NCL with granular osmiophilic deposits without palmitoyl protein thioesterase 1 deficiencyPeter C G Nijssen
Department of Neurology, St Elisabeth Hospital, Tilburg, The Netherlands
Brain Pathol 13:574-81. 2003..However, activities of these enzymes were within normal range in our patients. Thus we propose that a gene distinct from the cathepsin D and CLN1-CLN8 genes is responsible for this autosomal dominant form of ANCL...
Electroencephalography in autosomal dominant adult neuronal ceroid lipofuscinosisP C G Nijssen
Department of Neurology and Clinical Neurophysiology, St Elisabeth Hospital, 5000 LC Tilburg, The Netherlands
Clin Neurophysiol 120:1782-6. 2009..To describe the findings in 59 EEGs from six patients from three generations in a family with autosomal dominant adult neuronal ceroid lipofuscinosis (Parry disease), autopsy proven, with a follow up of 9-21 years...
