Research Topics
Species | Esther BrusseSummaryAffiliation: Erasmus MC Country: The Netherlands Publications
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Detail Information
Publications
Spinocerebellar ataxia associated with a mutation in the fibroblast growth factor 14 gene (SCA27): A new phenotypeEsther Brusse
Department of Neurology, Erasmus MC University Medical Center Rotterdam, The Netherlands
Mov Disord 21:396-401. 2006..Behavioral problems were also observed. Further investigations will have to determine the role of FGF14 in the pathogenesis of neurodegeneration and the frequency of this FGF14 mutation in SCA. (c) 2005 Movement Disorder Society...
Diagnosis and management of early- and late-onset cerebellar ataxiaE Brusse
Department of Neurology, Erasmus Medical Center, Rotterdam, The Netherlands
Clin Genet 71:12-24. 2007..An appropriate diagnosis is of utmost importance to such considerations as prognosis, genetic counselling and possible therapeutic implications...
A novel 16p locus associated with BSCL2 hereditary motor neuronopathy: a genetic modifier?Esther Brusse
Department of Neurology, Erasmus MC University Medical Center, P O Box 2040, 3000 CA, Rotterdam, The Netherlands
Neurogenetics 10:289-97. 2009..These results expand the clinical spectrum of HMN and suggest a digenic inheritance of HMN in this family with a BSCL2 mutation and a chromosome 16 locus likely contributing to the phenotype...
Fatigue in spinocerebellar ataxia: patient self-assessment of an early and disabling symptomEsther Brusse
Department of Neurology, Erasmus MC University Medical Center Rotterdam, PO Box 2040, 3000 CA, Rotterdam, The Netherlands
Neurology 76:953-9. 2011..To identify the prevalence and severity of fatigue and predicting factors for severe fatigue in autosomal dominant spinocerebellar ataxia (SCA)...
A mutation in the fibroblast growth factor 14 gene is associated with autosomal dominant cerebellar ataxia [corrected]John C van Swieten
Department of Neurology, Erasmus Medical Center, Rotterdam, The Netherlands
Am J Hum Genet 72:191-9. 2003..The present FGF14 mutation represents a novel gene defect involved in the neurodegeneration of cerebellum and basal ganglia...
Randomised controlled trial comparing two different intravenous immunoglobulins in chronic inflammatory demyelinating polyradiculoneuropathyK Kuitwaard
Department of Neurology, Erasmus MC, University Medical Center, Rotterdam, The Netherlands
J Neurol Neurosurg Psychiatry 81:1374-9. 2010..A liquid IVIg preparation is more user friendly and potentially can be infused at a faster rate...
Cortical brain malformations: effect of clinical, neuroradiological, and modern genetic classificationMarie Claire Yvette de Wit
Department of Pediatric Neurology, Erasmus Medical Center Sophia Children s Hospital, Rotterdam, The Netherlands
Arch Neurol 65:358-66. 2008..Much progress in understanding the genetic causes has been made recently. The number of affected children in whom a molecularly confirmed diagnosis can be made is unclear...
Autosomal dominant adult neuronal ceroid lipofuscinosis: parkinsonism due to both striatal and nigral dysfunctionPeter C G Nijssen
Department of Neurology, St Elisabeth Hospital, Tilburg, The Netherlands
Mov Disord 17:482-7. 2002..We conclude that parkinsonism in ANCL is likely to be caused by both presynaptic nigral cell loss and postsynaptic striatal degeneration...
