Research TopicsGenomes and GenesSpecies | Levinus A BokSummaryCountry: The Netherlands Publications
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Publications
Long-term outcome in pyridoxine-dependent epilepsyLevinus A Bok
Department of Pediatrics, Maxima Medical Center, Veldhoven, The Netherlands
Dev Med Child Neurol 54:849-54. 2012..The long-term outcome of the Dutch pyridoxine-dependent epilepsy cohort and correlations between patient characteristics and follow-up data were retrospectively studied...
Pyridoxine-dependent seizures in Dutch patients: diagnosis by elevated urinary alpha-aminoadipic semialdehyde levelsLevinus A Bok
Department of Paediatrics, Maxima Medical Center, Veldhoven, The Netherlands
Arch Dis Child 92:687-9. 2007..Recently alpha-aminoadipic semialdehyde (alpha-AASA) dehydrogenase deficiency was identified as a major cause of PDS, which causes accumulation of both alpha-AASA and pipecolic acid (PA) in body fluids...
Antenatal treatment in two Dutch families with pyridoxine-dependent seizuresLevinus A Bok
Department of Paediatrics, Maxima Medical Centre, P O Box 7777, 5500 MB, Veldhoven, The Netherlands
Eur J Pediatr 169:297-303. 2010..These results suggest that antenatal pyridoxine supplementation may be effective in preventing intrauterine seizures, decreasing the risk of complicated birth and improving neurodevelopmental outcome in PDS...
The EEG response to pyridoxine-IV neither identifies nor excludes pyridoxine-dependent epilepsyLevinus A Bok
Department of Pediatrics, Maxima Medical Center, Veldhoven, The Netherlands
Epilepsia 51:2406-11. 2010..Prompt recognition of PDE is important for treatment and prognosis of seizures. We aimed to determine whether immediate electroencephalography (EEG) alterations by pyridoxine-IV can identify PDE in neonates with TRS...
Lysine restricted diet for pyridoxine-dependent epilepsy: first evidence and future trialsClara D M van Karnebeek
Division of Biochemical Diseases, Department of Pediatrics, BC Children s Hospital, University of British Columbia, Vancouver, Canada
Mol Genet Metab 107:335-44. 2012....
Mutations in the ALDH7A1 gene cause pyridoxine-dependent seizuresJasper V Been
Arq Neuropsiquiatr 66:288; author reply 288-9. 2008
An intriguing "silent" mutation and a founder effect in antiquitin (ALDH7A1)Gajja S Salomons
Metabolic Unit, Department of Clinical Chemistry, VU University Medical Center, Amsterdam, The Netherlands
Ann Neurol 62:414-8. 2007..Here, we report an intriguing "silent" mutation in ALDH7A1, a novel missense mutation and a founder mutation in a Dutch cohort (10 patients) with alpha-AASA dehydrogenase deficiency...
Extensive cerebral infarction in the newborn due to incontinentia pigmentiFemke Maingay-de Groof
Neonatal Intensive Care Unit, Erasmus MC Sophia Rotterdam, The Netherlands
Eur J Paediatr Neurol 12:284-9. 2008..Vascular occlusive phenomena probably play a role in CNS involvement. Whether these vascular changes are based on macro- or microvascular disease in the neonatal presentation is not fully understood...
