Research Topics
Species | Xose M LensSummaryCountry: Spain Publications
| Collaborators
|
Detail Information
Publications
A novel pattern of mutation in uromodulin disorders: autosomal dominant medullary cystic kidney disease type 2, familial juvenile hyperuricemic nephropathy, and autosomal dominant glomerulocystic kidney diseaseXose M Lens
Laboratorio de Investigación en Nefroloxía, Complexo Hospitalario Universitario de Santiago, Santiago de Compostela, Spain
Am J Kidney Dis 46:52-7. 2005..Based on such mutation clustering, some investigators have proposed that the sequencing of UMOD exon 4 might become a preliminary diagnostic test for patients with this phenotype...
Homozygosity for uromodulin disorders: FJHN and MCKD-type 2Wânia Rezende-Lima
Laboratorio de Investigación en Nefroloxía, Complexo Hospitalario Universitario de Santiago, Santiago de Compostela, Spain
Kidney Int 66:558-63. 2004..Mutations of the UMOD gene, disrupting the tertiary structure of uromodulin, cause MCKD2 and FJHN...
Evaluating the clinical utility of a molecular genetic test for polycystic kidney diseaseMiguel A Garcia-Gonzalez
Johns Hopkins University School of Medicine, Department of Medicine, Division of Nephrology, Baltimore, MD 21205, USA, and Laboratorio de Investigación en Nefroloxía, Complexo Hospitalario Universitario de Santiago, Santiago de Compostela, Spain
Mol Genet Metab 92:160-7. 2007..We conclude that a significant fraction of ADPKD mutations are caused by amino acid substitutions that need to be interpreted carefully when utilized in clinical decision-making...
A novel mutation, outside of the candidate region for diagnosis, in the inverted formin 2 gene can cause focal segmental glomerulosclerosisMaria Sanchez-Ares
Laboratory of Nephrology, Sanitary Research Institute IDIS, Santiago de Compostela, Spain
Kidney Int 83:153-9. 2013..Thus, this novel mutation in INF2 linked to nonsyndromic FSGS indicates the necessity for full gene sequencing if no mutation is found in the current rapid-screen region of the gene...
