Research Topics
| Doris TahaSummaryAffiliation: King Faisal Specialist Hospital and Research Centre Country: Saudi Arabia Publications
| Collaborators
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Detail Information
Publications
Neonatal diabetes mellitus, congenital hypothyroidism, hepatic fibrosis, polycystic kidneys, and congenital glaucoma: a new autosomal recessive syndrome?Doris Taha
Division of Pediatric Endocrinology, King Faisal Specialist Hospital and Research Center, PO Box 40047, Jeddah 21499, Kingdom of Saudi Arabia
Am J Med Genet A 122:269-73. 2003..Mutation analysis for several candidate genes is warranted...
A novel VPS33B mutation in an ARC syndrome patient presenting with osteopenia and fractures at birthDoris Taha
Division of Pediatric Endocrinology, Department of Pediatrics, King Faisal Specialist Hospital and Research Centre-Jeddah, Kingdom of Saudi Arabia
Am J Med Genet A 143:2835-7. 2007
Hyperglycemia and hypoinsulinemia in patients with Fanconi-Bickel syndromeDoris Taha
Division of Pediatric Endocrinology, Department of Pediatrics, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia
J Pediatr Endocrinol Metab 21:581-6. 2008..Mutations in GLUT2, the gene for facilitative glucose transporter protein 2 (GLUT2), cause FBS...
The prevalence of metabolic syndrome and cardiovascular risk factors in a group of obese Saudi children and adolescents: a hospital-based studyDoris Taha
Department of Pediatrics, King Faisal Specialist Hospital and Research Centre, PO Box 40047, Jeddah 21499, Saudi Arabia
Ann Saudi Med 29:357-60. 2009..We assessed the distribution of risk factors associated with the metabolic syndrome in a group of obese Saudi children and adolescents. No previous studies had addressed this issue in the Saudi pediatric population...
Absent or delayed adrenarche in Pit-1/POU1F1 deficiencyDoris Taha
Department of Pediatrics, King Faisal Specialist Hospital and Research Centre Jeddah, Jeddah, Saudi Arabia
Horm Res 64:175-9. 2005..The absence/delay of adrenarche in POU1F1-deficient patients and the absence/delay of pubarche in POU1F1-deficient females suggest that a POU1F1-dependent factor contributes to the normal development of adrenarche and female pubarche...
Type 2 diabetes mellitus in African-American adolescents: impaired beta-cell function in the face of severe insulin resistanceDoris Taha
Department of Pediatrics, King Faisal Specialist Hospital and Research Centre, Jeddah, Saudi Arabia
J Pediatr Endocrinol Metab 19:135-42. 2006..4 +/- 0.8 vs 2.9 +/- 0.4; p = 0.0002). Adolescents with DM2 have dyslipidemia, a significant cardiovascular risk factor. Decreased beta-cell function is characteristic of adolescents with DM2 in the presence of severe insulin resistance...
Neonatal diabetes mellitus because of pancreatic agenesis with dysmorphic features and recurrent bacterial infectionsDoris Taha
Division of Pediatric Endocrinology, Department of Pediatrics, King Faisal Specialist Hospital and Research Centre Jeddah, Jeddah, Saudi Arabia
Pediatr Diabetes 9:240-4. 2008..The association of permanent neonatal diabetes because of pancreatic agenesis, dysmorphism, and non-specific immunodeficiency is previously undescribed and may represent a new possibly autosomal recessive syndrome...
Fatal lymphoproliferative disorder in a child with Schimke immuno-osseous dysplasiaDoris Taha
Department of Pediatrics, King Faisal Specialist Hospital and Research Centre Jeddah, Jeddah, Saudi Arabia
Am J Med Genet A 131:194-9. 2004..To our knowledge, this is the first report of an SIOD patient with a primary lymphoproliferative disorder (LPD)...
Arthrogryposis, renal tubular acidosis and cholestasis (ARC) syndrome: two new cases and reviewMaha Barbar
Division of General Pediatrics, Department of Pediatrics, King Faisal Specialist Hospital and Research Centre-Jeddah, Kingdom of Saudi Arabia
Clin Dysmorphol 14:191-6. 2005..We also review 39 ARC cases reported in the literature using the Medline database from January 1966 to September 2004...
Nephrocalcinosis in glucose-galactose malabsorption, association with renal tubular acidosisWalid El-Naggar
Department of Pediatrics, King Faisal Specialist Hospital and Research Centre-Jeddah, Jeddah, Kingdom of Saudi Arabia
Pediatr Nephrol 20:1336-9. 2005..Although GGM has been reported previously with nephrocalcinosis, this report is the first to show that renal tubular acidosis could explain the coexistence of nephrocalcinosis in patients with glucose galactose malabsorption...
Re: EIF2AK3 mutations in patients with Wolcott-Rallison syndromeDoris Taha
Ann Saudi Med 25:350; author reply 350. 2005
Mutations in GLIS3 are responsible for a rare syndrome with neonatal diabetes mellitus and congenital hypothyroidismValérie Senée
Institut Pasteur, Génétique des Maladies Infectieuses et Autoimmunes, 75015 Paris, France
Nat Genet 38:682-7. 2006..These results demonstrate a major role for GLIS3 in the development of pancreatic beta cells and the thyroid, eye, liver and kidney...
Schimke immunoosseous dysplasia: suggestions of genetic diversityJ Marietta Clewing
Department of Molecular and Human Genetics, Baylor College of Medicine, Houston, Texas, USA
Hum Mutat 28:273-83. 2007..This is the first evidence for nonallelic heterogeneity in SIOD. From analysis of the postmortem histopathology from two patients and the clinical data from most patients, we propose the existence of endophenotypes of SIOD...
Association of migraine-like headaches with Schimke immuno-osseous dysplasiaSara Sebnem Kilic
Department of Pediatrics, Division of Immunology, Uludag University Medical Faculty, , Turkey
Am J Med Genet A 135:206-10. 2005..We hypothesize that these headaches may arise from an intrinsic vascular, neuroimmune, or neurovascular defect resulting from loss of SMARCAL1 function...
Wolcott-Rallison Syndrome: clinical, genetic, and functional study of EIF2AK3 mutations and suggestion of genetic heterogeneityValérie Senée
Génétique des Maladies Infectieuses et Autoimmunes, INSERM E102, Institut Pasteur, Paris, France
Diabetes 53:1876-83. 2004....
Hyperlipidemia in children with type 2 diabetes mellitusDoris Taha
Department of Pediatrics, State University of New York Health Science Center at Brooklyn and Children Medical Center of Brooklyn, 11203, USA
J Pediatr Endocrinol Metab 15:505-7. 2002..When goals are not met, drug therapy should be considered...
