Research Topics
Species | Daniela MelisSummaryCountry: Italy Publications
| Collaborators
|
Detail Information
Publications
Mosaic 13q13.2-ter deletion restricted to tissues of ectodermal and mesodermal originsDaniela Melis
Department of Pediatrics, Federico II University, Naples, Italy
Clin Dysmorphol 15:13-8. 2006..We suggest analysing a fibroblast karyotype when a diagnosis of 13q- syndrome is suspected on clinical ground. The role of teratogens in causing this type of mosaic chromosome abnormality also warrants further investigation...
NPT4, a new microsomal phosphate transporter: mutation analysis in glycogen storage disease type IcD Melis
Department of Clinical Genetics, Erasmus University Rotterdam, The Netherlands
J Inherit Metab Dis 27:725-33. 2004..Our results do not confirm the hypothesis that this gene is mutated in GSD Ic patients. However, we cannot exclude that the mutation found reduces the phosphate transport efficiency, possibly modulating the G6-Pase complex...
Genotype/phenotype correlation in glycogen storage disease type 1b: a multicentre study and review of the literatureDaniela Melis
Dipartimento di Pediatria, Universita Federico II, Via Sergio Pansini 5, 80131 Napoli, Italy
Eur J Pediatr 164:501-8. 2005..The absence of detectable mutations in three patients could suggest that a second protein plays a role in microsomal phosphate transport...
Efficacy of ACE-inhibitor therapy on renal disease in glycogen storage disease type 1: a multicentre retrospective studyD Melis
Dipartimento di Pediatria, Universita Federico II, Napoli, Italy
Clin Endocrinol (Oxf) 63:19-25. 2005..The efficacy of ACE-inhibitors in decreasing microalbuminuria and proteinuria has been reported in a few patients with glycogen storage disease type 1 (GSD1); however, no case-control study has ever been published...
Mutation spectrum of MLL2 in a cohort of Kabuki syndrome patientsLucia Micale
Medical Genetics Unit, IRCCS Casa Sollievo della Sofferenza Hospital, 71013 San Giovanni Rotondo, Italy
Orphanet J Rare Dis 6:38. 2011..Recently mutations in the histone methyl transferase MLL2 gene have been identified as its underlying cause...
The growth hormone-insulin-like growth factor axis in glycogen storage disease type 1: evidence of different growth patterns and insulin-like growth factor levels in patients with glycogen storage disease type 1a and 1bDaniela Melis
Department of Pediatrics, Federico II University, Naples, Italy
J Pediatr 156:663-70.e1. 2010..To investigate the growth hormone (GH)-insulin-like growth factor (IGF) system in patients with glycogen storage disease type 1 (GSD1)...
Clinical description of a patient carrying the smallest reported deletion involving 10p14 regionDaniela Melis
Department of Paediatrics, Federico II University, Naples, Italy
Am J Med Genet A 158:832-5. 2012..We also underline the importance of CGH-array, in order to obtain a more precise physical mapping of the 10p deletions and an accurate genotype-phenotype correlation...
Selective cognitive impairment and tall stature due to chromosome 19 supernumerary ringDaniela Melis
Department of Pediatrics, Federico II University, Naples, Italy
Clin Dysmorphol 21:27-32. 2012..2002; Novelli et al., 2005; Vraneković et al., 2008). Herein, we report the phenotype and molecular cytogenetic analysis in a patient with the smallest de-novo constitutional ring extended from the p12 to q12 region of chromosome 19...
Increased prevalence of thyroid autoimmunity and hypothyroidism in patients with glycogen storage disease type IDaniela Melis
Department of Pediatrics, Federico II University, Naples, Italy
J Pediatr 150:300-5, 305.e1. 2007..To investigate the hypothalamus-pituitary-thyroid axis in patients with glycogen storage disease type 1(GSD1)...
Variegated silencing through epigenetic modifications of a large Xq region in a case of balanced X;2 translocation with Incontinentia Pigmenti-like phenotypeRita Genesio
Cellular and Molecular Biology and Pathology Department University of Naples Federico II, Naples, Italy
Epigenetics 6:1242-7. 2011..In conclusion, the study provides new insight into long-range gene silencing mechanisms and their direct impact in human disease...
Brain damage in glycogen storage disease type IDaniela Melis
Department of Pediatrics, , Naples, Italy
J Pediatr 144:637-42. 2004..05). CONCLUSIONS: Brain damage, probably caused by recurrent severe hypoglycemia, may be present in patients with GSDI...
Fulminant autoimmune hepatitis in a girl with 22q13 deletion syndrome: a previously unreported associationMaria Tufano
Pediatric Liver Unit, Department of Pediatrics, University of Naples Federico II, Via S Pansini 5, 80131 Naples, Italy
Eur J Pediatr 168:225-7. 2009..This is the first case of fulminant autoimmune hepatitis associated with the 22q13 deletion syndrome. The possible relationships between immune system dysfunctions peculiar of this syndrome and autoimmune hepatitis are discussed...
A further contribution to the delineation of the 17q21.31 microdeletion syndrome: central nervous involvement in two Italian patientsGaetano Terrone
Department of Pediatrics, Federico II University, via Pansini N 5, Naples, Italy
Eur J Med Genet 55:466-71. 2012..This malformation should be considered in patients with the 17q21.31 microdeletion syndrome, presenting suggestive symptoms (headache, neck pain, cerebellar signs or muscle weakness)...
Nephrological findings and genotype-phenotype correlation in Beckwith-Wiedemann syndromeAlessandro Mussa
Department of Pediatrics, University of Torino, Piazza Polonia 94, 10126, Torino, Italy
Pediatr Nephrol 27:397-406. 2012..9% of patients, with two resulting in life-threatening sepsis. Hypercalciuria was present in 10% of cases. 55.5% of BWS patients have renal findings. Although variegate, these anomalies disclose a genotype-phenotype correlation...
Mental retardation, congenital heart malformation, and myelodysplasia in a patient with a complex chromosomal rearrangement involving the critical region 21q22Daniela Melis
Department of Paediatrics, Federico II University, Naples, Italy
Am J Med Genet A 155:1697-705. 2011..The present report underlines also the importance of array-CGH in characterizing patients with a complex phenotype...
Trisomy 18 and hypertrophy cardiomyopathy in an 18-year-old womanGiuseppe Limongelli
Department of Cardiology, Monaldi Hospital, Second University of Naples, Naples, Italy
Am J Med Genet A 146:327-9. 2008
A new familial case of spondylo-epi-metaphyseal dysplasia with multiple dislocations Hall type (leptodactylic form)Massimiliano Rossi
Department of Pediatrics, Federico II University, Naples, Italy
Clin Dysmorphol 14:13-8. 2005..This family contributes to the delineation of the clinical and radiological phenotype of this rare condition...
