Research Topics
Genomes and GenesSpecies | Alberto MartiniSummaryAffiliation: G. Gaslini Institute Country: Italy Publications
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Publications
Systemic juvenile idiopathic arthritisAlberto Martini
Dipartimento di Pediatria, Universita di Genova, Pediatria II e Reumatologia, Istituto G Gaslini, Genova, Italy
Autoimmun Rev 12:56-9. 2012..The specific inhibition of these two cytokines is going to change not only the therapeutic approach to the disease but also, presumably, its long term prognosis...
It is time to rethink juvenile idiopathic arthritis classification and nomenclatureAlberto Martini
University of Genoa, Pediatria II, Istituto G Gaslini, Largo Gaslini 5, Genova 16147, Italy
Ann Rheum Dis 71:1437-9. 2012..Recent advances have shown that while some JIA categories identify quite definite disease entities, others still include heterogeneous conditions. Some aspects of JIA classification and nomenclature need therefore to be reconsidered...
JIA in 2011: New takes on categorization and treatmentAlberto Martini
University of Genoa, Pediatria II e Reumatologia, Istituto G Gaslini, Largo G Gaslini 5, 16147 Genoa, Italy
Nat Rev Rheumatol 8:67-8. 2012..These advances hold promise for improved management of JIA in 2012 and beyond...
Juvenile idiopathic arthritis: state of the art and future perspectivesAlberto Martini
Dipartimento di Pediatria, Universita di Genova, Pediatria II Reumatologia, IRCCS G Gaslini, Largo Gaslini 5, 16147 Genova, Italy
Ann Rheum Dis 69:1260-3. 2010..However, despite a dramatic advance in the understanding of JIA categories, pathobiology and treatments, much remains to be done...
Agreement between multi-dimensional and renal-specific response criteria in patients with juvenile systemic lupus erythematosus and renal diseaseNicolino Ruperto
IRCCS G Gaslini, Pediatria II, Reumatologia, Paediatric Rheumatology INternational Trials Organisation PRINTO, Genova, Italy
Clin Exp Rheumatol 28:424-33. 2010..To evaluate change over time and level of agreement of renal-specific and multi-dimensional measures in juvenile systemic lupus erythematosus (SLE) with renal disease...
Phenotypic and functional characterization of switch memory B cells from patients with oligoarticular juvenile idiopathic arthritisAnna Corcione
Laboratory of Oncology, IRCCS G Gaslini, Largo G Gaslini 5, Genoa, 16148, Italy
Arthritis Res Ther 11:R150. 2009..Here, we have characterized synovial fluid and tissue B-cell subsets in patients with oligoarticular juvenile idiopathic arthritis (JIA), an issue not addressed before in detail...
Validation of the Childhood Health Assessment Questionnaire in active juvenile systemic lupus erythematosusSilvia Meiorin
IRCCS G Gaslini, Pediatria II, Reumatologia and Paediatric Rheumatology International Trials Organisation, Universita di Genova, Largo Gaslini 5, Genoa, Italy
Arthritis Rheum 59:1112-9. 2008..To validate the Childhood Health Assessment Questionnaire (C-HAQ) as a measure of disability in patients with active juvenile systemic lupus erythematosus (SLE)...
Development and testing of reduced joint counts in juvenile idiopathic arthritisAnna Bazso
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Largo G Gaslini 5, 16147 Genova, Italy
J Rheumatol 36:183-90. 2009..To develop and test reduced joint counts in children with juvenile idiopathic arthritis (JIA)...
Development and preliminary validation of a paediatric-targeted MRI scoring system for the assessment of disease activity and damage in juvenile idiopathic arthritisClara Malattia
Correspondence to Dr Clara Malattia, Pediatria II, IRCCS G Gaslini, Largo G Gaslini 5, 16147 Genova, Italy
Ann Rheum Dis 70:440-6. 2011..To compare the paediatric MRI score with the adult-designed. Outcome Measures in Rheumatology Clinical Trials-Rheumatoid Arthritis MRI Score (RAMRIS), whose suitability for assessing growing joints was tested...
Development and initial validation of a radiographic scoring system for the hip in juvenile idiopathic arthritisMarta Bertamino
Universita degli Studi di Genova, Genova, Italy
J Rheumatol 37:432-9. 2010..To develop and validate a radiographic scoring system for the assessment of radiographic damage in the hip joint in patients with juvenile idiopathic arthritis (JIA)...
Dynamic contrast-enhanced magnetic resonance imaging in the assessment of disease activity in patients with juvenile idiopathic arthritisClara Malattia
Pediatria II, IRCCS G Gaslini, Largo G Gaslini 5, 16147 Genova, Italy
Rheumatology (Oxford) 49:178-85. 2010..To determine the capability and reliability of dynamic contrast-enhanced MRI (DCE-MRI) in the assessment of disease activity in juvenile idiopathic arthritis (JIA)...
Evaluation of 21-numbered circle and 10-centimeter horizontal line visual analog scales for physician and parent subjective ratings in juvenile idiopathic arthritisGiovanni Filocamo
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Genova, Italy
J Rheumatol 37:1534-41. 2010..To evaluate the measurement properties of 21-numbered circle visual analog scales (VAS) and traditional 10-cm horizontal line VAS for physician and parent subjective ratings in children with juvenile idiopathic arthritis (JIA)...
Remission, minimal disease activity, and acceptable symptom state in juvenile idiopathic arthritis: defining criteria based on the juvenile arthritis disease activity scoreAlessandro Consolaro
Istituto G Gaslini, Genoa, Italy
Arthritis Rheum 64:2366-74. 2012..To determine cutoff values for defining remission, minimal disease activity, and parent and child acceptable symptom state in juvenile idiopathic arthritis (JIA) using the Juvenile Arthritis Disease Activity Score (JADAS)...
Physicians' and parents' ratings of inactive disease are frequently discordant in juvenile idiopathic arthritisAlessandro Consolaro
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Genova, Italy
J Rheumatol 34:1773-6. 2007..To investigate discrepancies between physicians' and parents' ratings of inactive disease in children with juvenile idiopathic arthritis (JIA) and the determinants of the discrepancy...
Long-term efficacy and safety of infliximab plus methotrexate for the treatment of polyarticular-course juvenile rheumatoid arthritis: findings from an open-label treatment extensionNicolino Ruperto
IRCCS Istituto G Gaslini, Pediatria II PRINTO, Largo Gaslini 5, EULAR Centre of Excellence in Rheumatology 2008 13, Genoa, Italy
Ann Rheum Dis 69:718-22. 2010..To assess the long-term efficacy and safety of infliximab plus methotrexate in juvenile rheumatoid arthritis (JRA)...
Proxy-reported health-related quality of life of patients with juvenile idiopathic arthritis: the Pediatric Rheumatology International Trials Organization multinational quality of life cohort studySheila Oliveira
IRCCS G Gaslini, Pediatria II, Reumatologia, Pediatric Rheumatology International Trials Organization, Genoa, Italy
Arthritis Rheum 57:35-43. 2007..To investigate the proxy-reported health-related quality of life (HRQOL) and its determinants in patients with juvenile idiopathic arthritis (JIA)...
Course of joint disease in patients with antinuclear antibody-positive juvenile idiopathic arthritisEnrico Felici
Dipartimento di Pediatria, , , Istituto di Ricovero e Cura a Carattere Scientifico G. Gaslini, Genova, Italy
J Rheumatol 32:1805-10. 2005..The early occurrence of ankle and/or wrist disease may indicate a higher likelihood of arthritis progression...
Parent and child acceptable symptom state in juvenile idiopathic arthritisGiovanni Filocamo
Pediatria II, Istituto G Gaslini, Largo G Gaslini 5, 16147 Genoa, Italy
J Rheumatol 39:856-63. 2012..To explore the parent and child acceptable symptom state in juvenile arthritis (JA-PASS and JA-CASS, respectively) and estimate the JA-PASS and JA-CASS cutoff values for outcome measures...
Clinical impact of MEFV mutations in children with periodic fever in a prevalent western European Caucasian populationSilvia Federici
UO Pediatria II Reumatologia, Istituto G Gaslini, Genova, Italy
Ann Rheum Dis 71:1961-5. 2012..To evaluate the actual impact of MEFV mutations on clinical manifestations associated with fever attacks in Caucasian children with periodic fever...
Achievement of a state of inactive disease at least once in the first 5 years predicts better outcome of patients with polyarticular juvenile idiopathic arthritisAlessandra Magnani
Istituto G Gaslini, Largo G Gaslini 5, 16147 Genova, Italy
J Rheumatol 36:628-34. 2009..To investigate whether the achievement of inactive disease in the first 5 years predicts a more favorable outcome of children with juvenile idiopathic arthritis (JIA)...
Criteria to define response to therapy in paediatric rheumatic diseasesNicolino Ruperto
IRCCS G Gaslini, Pediatria II, Reumatologia, Pædiatric Rheumatology International Trials Organisation PRINTO, Genoa, Italy
Eur J Clin Pharmacol 67:125-31. 2011....
Periodic fever, apthous stomatitis, pharyngitis and adenitis syndromeRoberta Caorsi
UO Pediatria II, G Gaslini Institute and Department of Pediatrics, University of Genoa, Genoa, Italy
Curr Opin Rheumatol 22:579-84. 2010..We report on the findings coming from the analysis of large cohorts of PFAPA patients and the possible implication for the differential diagnosis. An update on the efficacy of possible prophylactic treatments and tonsillectomy is given...
Toward a treat-to-target approach in the management of juvenile idiopathic arthritisAlessandro Consolaro
Istituto di Ricovero e Cura a Carattere Scientifico Giannina Gaslini, Genova, Italy
Clin Exp Rheumatol 30:S157-62. 2012..Future studies will clarify whether the addition of an imaging assessment to the management of children with JIA will improve the prediction of clinical outcomes...
Therapeutic approaches in the treatment of juvenile dermatomyositis in patients with recent-onset disease and in those experiencing disease flare: an international multicenter PRINTO studyRachana Hasija
IRCCS G Gaslini, Genoa, Italy
Arthritis Rheum 63:3142-52. 2011..To evaluate response to therapy over a 24-month period in a large prospective international cohort of patients with juvenile dermatomyositis (DM)...
Comparison of clinical features and drug therapies among European and Latin American patients with juvenile dermatomyositisDinara Guseinova
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Genova, Italy
Clin Exp Rheumatol 29:117-24. 2011..To compare the demographic features, presenting manifestations, diagnostic investigations, disease course, and drug therapies of children with juvenile dermatomyositis (JDM) followed in Europe and Latin America...
A new short and simple health-related quality of life measurement for paediatric rheumatic diseases: initial validation in juvenile idiopathic arthritisGiovanni Filocamo
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Genova, Italy
Rheumatology (Oxford) 49:1272-80. 2010..To develop and validate a new short and simple measure of health-related quality of life (HRQL) in children with juvenile idiopathic arthritis (JIA)...
The hypoxic synovial environment regulates expression of vascular endothelial growth factor and osteopontin in juvenile idiopathic arthritisMaria Carla Bosco
Laboratory of Molecular Biology, Department of Pediatrics, G Gaslini Institute, Genova, Italy
J Rheumatol 36:1318-29. 2009..We characterized the contribution of the local hypoxic environment to VEGF and OPN production by monocytic cells recruited to the synovium in JIA...
An international consensus survey of diagnostic criteria for macrophage activation syndrome in systemic juvenile idiopathic arthritisSergio Davì
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Genova, Italy
J Rheumatol 38:764-8. 2011..To identify candidate diagnostic criteria for macrophage activation syndrome (MAS) complicating systemic juvenile idiopathic arthritis (sJIA) using international consensus formation through a Delphi questionnaire survey...
A new approach to clinical care of juvenile idiopathic arthritis: the Juvenile Arthritis Multidimensional Assessment ReportGiovanni Filocamo
Pediatria II, Istituto G Gaslini, Largo G Gaslini 5, Genoa, Italy
J Rheumatol 38:938-53. 2011..To develop and test a new multidimensional questionnaire for assessment of children with juvenile idiopathic arthritis (JIA) in standard clinical care...
Differentiating PFAPA syndrome from monogenic periodic feversMarco Gattorno
UO Pediatria II, G Gaslini Institute, Largo G Gaslini 5, 16146, Genova, Italy
Pediatrics 124:e721-8. 2009....
EULAR/PRINTO/PRES criteria for Henoch-Schönlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arteritis: Ankara 2008. Part I: Overall methodology and clinical characterisationNicolino Ruperto
Paediatric Rheumatology INternational Trials Organisation PRINTO, IRCCS G Gaslini, Universita di Genova, Pediatria II Reumatologia, EULAR Centre of Excellence in Rheumatology 2008 2013, Largo Gaslini, 5, Genova 16147, Italy
Ann Rheum Dis 69:790-7. 2010....
Treatment of Takayasu's arteritis with tumor necrosis factor antagonistsGiovanni Filocamo
Pediatria II IRCCS G Gaslini e Dipartimento di Pediatria, Universita di Genova, Italy
J Pediatr 153:432-4. 2008..Two patients went into remission; in the other 2, the response was partial. Anti-tumor necrosis factor agents can have a role in the treatment of Takayasu's arteritis; further controlled studies are required...
Consensus procedures and their role in pediatric rheumatologyNicolino Ruperto
IRCCS G Gaslini, Pediatria II PRINTO, University of Genoa, Largo Gaslini, 5, 16147 Genova, Italy
Curr Rheumatol Rep 10:142-6. 2008....
The Pediatric Rheumatology International Trials Organization/American College of Rheumatology provisional criteria for the evaluation of response to therapy in juvenile systemic lupus erythematosus: prospective validation of the definition of improvementNicolino Ruperto
Pediatric Rheumatology International Trials Organization, IRCCS G Gaslini, Università di Genova Pediatria II Reumatologia, 5 Largo Gaslini, 16147 Genoa, Italy
Arthritis Rheum 55:355-63. 2006....
Predictors of poor response to methotrexate in polyarticular-course juvenile idiopathic arthritis: analysis of the PRINTO methotrexate trialIris Vilca
IRCCS G Gaslini, Pediatria II, Reumatologia, PRINTO, Genova, Italy
Ann Rheum Dis 69:1479-83. 2010..To determine whether baseline demographic, clinical, articular and laboratory variables predict methotrexate (MTX) poor response in polyarticular-course juvenile idiopathic arthritis...
Abatacept improves health-related quality of life, pain, sleep quality, and daily participation in subjects with juvenile idiopathic arthritisNicolino Ruperto
Universita di Genova, Genoa, Italy
Arthritis Care Res (Hoboken) 62:1542-51. 2010..To assess health-related quality of life (HRQOL) in abatacept-treated children/adolescents with juvenile idiopathic arthritis (JIA)...
Abatacept in children with juvenile idiopathic arthritis: a randomised, double-blind, placebo-controlled withdrawal trialNicolino Ruperto
IRCCS G Gaslini, PRINTO, Genoa, Italy
Lancet 372:383-91. 2008..We aimed to assess the safety and efficacy of abatacept, a selective T-cell costimulation modulator, in children with juvenile idiopathic arthritis who had failed previous treatments...
A proposal for a pediatric version of the Systemic Lupus International Collaborating Clinics/American College of Rheumatology Damage Index based on the analysis of 1,015 patients with juvenile-onset systemic lupus erythematosusRaul Gutiérrez-Suárez
IRCCS G Gaslini, Genoa, Italy
Arthritis Rheum 54:2989-96. 2006....
Performance of Birmingham Vasculitis Activity Score and disease extent index in childhood vasculitidesErkan Demirkaya
IRCCS G Gaslini, Pediatria II, Reumatologia, PRINTO, Genova, Italy
Clin Exp Rheumatol 30:S162-8. 2012..To evaluate the performance of the Birmingham Vasculitis Activity Score (BVAS) v3 and the Disease Extent Index (DEI) for the assessment of disease activity in 4 primary childhood (c-) systemic vasculitides...
Agreement between physicians and parents in rating functional ability of children with juvenile idiopathic arthritisElena Palmisani
Pediatria II, Istituto di Ricovero e Cura a Carattere Scientifico G, Gaslini, Genova, Italy
Pediatr Rheumatol Online J 5:23. 2007..To investigate concordance between physicians and parents in rating the degree of functional ability of children with juvenile idiopathic arthritis (JIA)...
Adapted versions of the Sharp/van der Heijde score are reliable and valid for assessment of radiographic progression in juvenile idiopathic arthritisAngelo Ravelli
Università degli Studi di Genoa, and IRCCS, Istituto G Gaslini, Genoa, Italy
Arthritis Rheum 56:3087-95. 2007..To develop adapted versions of the Sharp/van der Heijde radiographic scoring system for use in juvenile idiopathic arthritis (JIA), and to investigate their validity in JIA patients with polyarticular disease...
A randomized, placebo-controlled trial of infliximab plus methotrexate for the treatment of polyarticular-course juvenile rheumatoid arthritisNicolino Ruperto
IRCCS, Istituto G Gaslini, Genoa, Italy
Arthritis Rheum 56:3096-106. 2007..To evaluate the safety and efficacy of infliximab in the treatment of juvenile rheumatoid arthritis (JRA)...
A phase II, multicenter, open-label study evaluating dosing and preliminary safety and efficacy of canakinumab in systemic juvenile idiopathic arthritis with active systemic featuresNicolino Ruperto
IRCCS G Gaslini, Genoa, Italy
Arthritis Rheum 64:557-67. 2012..To assess dosing, preliminary safety, and efficacy of canakinumab, a fully human anti-interleukin-1β (anti-IL-1β) antibody, in children with systemic juvenile idiopathic arthritis (JIA) and active systemic features...
Network in pediatric rheumatology: the example of the Pediatric Rheumatology International Trials OrganizationNicolino Ruperto
IRCCS Istituto G Gaslini, Pediatria II, Reumatologia, Genoa, Italy
World J Pediatr 4:186-91. 2008..The research aimed at studying new therapeutic approaches is difficult because of logistic, methodological and ethical problems...
Magnetic resonance imaging, ultrasonography, and conventional radiography in the assessment of bone erosions in juvenile idiopathic arthritisClara Malattia
Istituto G Gaslini, Genoa, Italy
Arthritis Rheum 59:1764-72. 2008....
Level of agreement between children, parents, and physicians in rating pain intensity in juvenile idiopathic arthritisPablo Garcia-Munitis
, Istituto di Ricovero e Cura a Carattere Scientifico G. Gaslini, , Largo G. Gaslini 5, 16147 Genoa, Italy
Arthritis Rheum 55:177-83. 2006..The intensity of pain was the strongest determinant of discordance between children and other raters...
Preliminary diagnostic guidelines for macrophage activation syndrome complicating systemic juvenile idiopathic arthritisAngelo Ravelli
Department of Pediatrics, Division of Pediatrics II, University of Genoa, Istituto G Gaslini, Largo G Gaslini 5, 16147 Genoa, Italy
J Pediatr 146:598-604. 2005..To develop diagnostic guidelines for macrophage activation syndrome (MAS) complicating systemic juvenile idiopathic arthritis (S-JIA)...
The Pediatric Rheumatology International Trials Organization criteria for the evaluation of response to therapy in juvenile systemic lupus erythematosus: prospective validation of the disease activity core setNicolino Ruperto
Pediatric Rheumatology International Trials Organization PRINTO, IRCCS G Gaslini, Universita di Genova, Pediatria II Reumatologia, Largo Gaslini, Genoa, Italy
Arthritis Rheum 52:2854-64. 2005..To validate and promulgate a core set of outcome measures for the evaluation of response to treatment in patients with juvenile systemic lupus erythematosus (SLE)...
Networking in paediatrics: the example of the Paediatric Rheumatology International Trials Organisation (PRINTO)Nicolino Ruperto
Pediatria II, Reumatologia, University of Genoa, EULAR Centre of Excellence in Rheumatology 2008 13, IRCCS G Gaslini, Largo G Gaslini 5, Genoa, Italy
Arch Dis Child 96:596-601. 2011..The PRINTO and PRCSG networks can be seen as a model for international co-operation in other paediatric subspecialties...
Health-related quality of life in juvenile-onset systemic lupus erythematosus and its relationship to disease activity and damageNicolino Ruperto
, Istituto di Ricovero e Cura a Carattere Scientifico G. Gaslini, Genoa, Italy
Arthritis Rheum 51:458-64. 2004..HRQL may be affected by both disease activity and accumulated damage, particularly in the renal, central nervous, and musculoskeletal systems...
Development and validation of a clinical index for assessment of long-term damage in juvenile idiopathic arthritisStefania Viola
, IRCCS G. Gaslini, Genoa, Italy
Arthritis Rheum 52:2092-102. 2005....
The PRINTO criteria for clinically inactive disease in juvenile dermatomyositisDragana Lazarevic
Correspondence to Nicolino Ruperto, Istituto Giannina Gaslini, Pediatria II, Reumatologia, PRINTO, Largo Gaslini 5, Genova 16147, Italy
Ann Rheum Dis 72:686-93. 2013..To develop data-driven criteria for clinically inactive disease on and off therapy for juvenile dermatomyositis (JDM)...
MRI of the wrist in juvenile idiopathic arthritis: proposal of a paediatric synovitis score by a consensus of an international working group. Results of a multicentre reliability studyMaria Beatrice Damasio
Department of Radiology, Ospedale Pediatrico Gaslini, Genova, Italy
Pediatr Radiol 42:1047-55. 2012..MRI is a sensitive tool for the evaluation of synovitis in juvenile idiopathic arthritis (JIA)...
Bone marrow-derived mesenchymal stem cells induce both polyclonal expansion and differentiation of B cells isolated from healthy donors and systemic lupus erythematosus patientsElisabetta Traggiai
Second Division of Pediatrics, IRCCS, Institute G Gaslini, Genova, Italy
Stem Cells 26:562-9. 2008..This study casts important questions on bone marrow mesenchymal stem cells as a therapeutic tool in autoimmune diseases in which B-cell activation is crucially implicated in the pathogenesis of the disease...
Successful treatment of idiopathic recurrent pericarditis in children with interleukin-1beta receptor antagonist (anakinra): an unrecognized autoinflammatory disease?Paolo Picco
G Gaslini Institute, University of Genoa, Genoa, Italy
Arthritis Rheum 60:264-8. 2009..The findings in these patients suggest that idiopathic recurrent pericarditis may be a previously unrecognized autoinflammatory disease...
Synovial and inflammatory diseases in childhood: role of new imaging modalities in the assessment of patients with juvenile idiopathic arthritisMaria Beatrice Damasio
Department of Diagnostic Imaging, G Gaslini Institute, Largo G Gaslini 5, Genoa 16148, Italy
Pediatr Radiol 40:985-98. 2010..In this era of advancing imaging technology, knowledge of the relative values of available imaging techniques is necessary to optimize the management of children with JIA...
HLA-G and HLA-E in patients with juvenile idiopathic arthritisIgnazia Prigione
Laboratory of Oncology, G Gaslini Scientific Institute, Largo G Gaslini 5, 16148 Genova, Italy
Rheumatology (Oxford) 50:966-72. 2011..To investigate the expression and release of HLA-G and HLA-E in JIA...
Pattern of interleukin-1beta secretion in response to lipopolysaccharide and ATP before and after interleukin-1 blockade in patients with CIAS1 mutationsMarco Gattorno
Second Division of Pediatrics, IRCCS, Istituto G Gaslini, Genoa, Italy
Arthritis Rheum 56:3138-48. 2007....
Emerging drugs to treat juvenile idiopathic arthritisNicolino Ruperto
IRCCS Istituto G Gaslini Pediatria II, Reumatologia, Genova, Italy
Expert Opin Emerg Drugs 16:493-505. 2011..Some of the new drugs that are under investigation for RA could also be suitable in the future for improving the treatment of JIA...
Two randomized trials of canakinumab in systemic juvenile idiopathic arthritisNicolino Ruperto
Istituto Giannina Gaslini, Pediatria II, Reumatologia, Paediatric Rheumatology International Trials Organisation PRINTO Coordinating Center, Genoa, Italy
N Engl J Med 367:2396-406. 2012..Interleukin-1 is pivotal in the pathogenesis of systemic juvenile idiopathic arthritis (JIA). We assessed the efficacy and safety of canakinumab, a selective, fully human, anti-interleukin-1β monoclonal antibody, in two trials...
Candidate genes in patients with autoinflammatory syndrome resembling tumor necrosis factor receptor-associated periodic syndrome without mutations in the TNFRSF1A geneSilvia Borghini
Laboratorio di Genetica Molecolare, Istituto G Gaslini, Genova, Italy
J Rheumatol 38:1378-84. 2011..Patients display different mutations of the TNF receptor superfamily 1A gene (TNFRSF1A), coding for a nearly ubiquitous TNF receptor (TNFR1). No TNFRSF1A mutation has been identified in a proportion of patients with TRAPS-like phenotype...
A randomized, double-blind, placebo-controlled trial of paracetamol and ketoprofren lysine salt for pain control in children with pharyngotonsillitis cared by family pediatriciansNicolino Ruperto
IRCCS G Gaslini, Pediatria II, Reumatologia, PRINTO, Genoa, Italy
Ital J Pediatr 37:48. 2011..To evaluate the analgesic effect and tolerability of paracetamol syrup compared to placebo and ketoprofen lysine salt in children with pharyngotonsillitis cared by family pediatricians...
Clinical assessment in juvenile dermatomyositisAngelo Ravelli
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Universita di Genova, Dipartimento di Pediatria, Italy
Autoimmunity 39:197-203. 2006....
The pattern of response to anti-interleukin-1 treatment distinguishes two subsets of patients with systemic-onset juvenile idiopathic arthritisMarco Gattorno
G Gaslini Institute, Genoa, Italy
Arthritis Rheum 58:1505-15. 2008..To assess the clinical response to interleukin-1 (IL-1) blockade and in vitro IL-1beta and IL-18 secretion in patients with systemic-onset juvenile idiopathic arthritis (JIA)...
Long-term outcome and prognostic factors of juvenile dermatomyositis: a multinational, multicenter study of 490 patientsAngelo Ravelli
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini and Università degli Studi di Genoa, Genoa, Italy
Arthritis Care Res (Hoboken) 62:63-72. 2010..To investigate the long-term outcome and prognostic factors of juvenile dermatomyositis (DM) through a multinational, multicenter study...
Diagnosis and management of autoinflammatory diseases in childhoodMarco Gattorno
2nd Division of Pediatrics, G Gaslini Scientific Institute, Largo G Gaslini 5, 16147, Genova, Italy
J Clin Immunol 28:S73-83. 2008..In the present review, we will focus on the clinical presentation of these disorders in childhood and report on the available therapeutic strategies...
Long-term safety and efficacy of abatacept in children with juvenile idiopathic arthritisNicolino Ruperto
Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Genoa, Italy
Arthritis Rheum 62:1792-802. 2010..Here, we report results from the long-term extension (LTE) phase of that study...
Increased expression of alpha(1,3)-fucosyltransferase-VII and P-selectin binding of synovial fluid T cells in juvenile idiopathic arthritisFabrizio De Benedetti
Pediatria Generale e Reumatologia, Dipartimento di Pediatria, IRCCS Policlinico San Matteo, Pavia, Italy
J Rheumatol 30:1611-5. 2003..CONCLUSION: Our data indicate an important role of FucT-VII in the enhanced homing of T cells to the inflamed synovium...
Juvenile idiopathic arthritisAngelo Ravelli
Department of Paediatrics, University of Genoa and Institute G Gaslini, Genoa, Italy
Lancet 369:767-78. 2007....
Preliminary core sets of measures for disease activity and damage assessment in juvenile systemic lupus erythematosus and juvenile dermatomyositisNicolino Ruperto
IRCCS G Gasalini, Pediatria II, Genova, Italy
Rheumatology (Oxford) 42:1452-9. 2003..To identify preliminary core sets of outcome variables for disease activity and damage assessment in juvenile systemic lupus erythematosus (JSLE) and juvenile dermatomyositis (JDM)...
Antinuclear antibody-positive patients should be grouped as a separate category in the classification of juvenile idiopathic arthritisAngelo Ravelli
IRCCS G Gaslini and Università degli Studi di Genova, Genoa, Italy
Arthritis Rheum 63:267-75. 2011....
The Paediatric Rheumatology International Trials Organisation provisional criteria for the evaluation of response to therapy in juvenile dermatomyositisNicolino Ruperto
Paediatric Rheumatology International Trials Organisation, Genoa, Italy
Arthritis Care Res (Hoboken) 62:1533-41. 2010..To develop a provisional definition for the evaluation of response to therapy in juvenile dermatomyositis (DM) based on the Paediatric Rheumatology International Trials Organisation juvenile DM core set of variables...
HRCT and pulmonary function tests in monitoring of lung involvement in juvenile systemic sclerosisSerena Panigada
U O Pneumologia, IRCCS G Gaslini, Genova, Italy
Pediatr Pulmonol 44:1226-34. 2009..To investigate the role of high-resolution computed tomography (HRCT) and pulmonary function tests (PFTs) in staging pulmonary involvement in juvenile systemic sclerosis (JSS)...
Coxarthritis as the presenting symptom of Gaucher disease type 1Giacomo Brisca
2nd Division of Paediatrics, G Gaslini Institute, Largo Gaslini 5, 16129 Genova, Italy
Arthritis 2011:361279. 2011..Herein, we report a patient in whom the osteoarticular involvement has been the only symptom of the disease stressing that this unusual presentation of GD has prompted a wide differential diagnosis with more common forms of coxitis...
The provisional Paediatric Rheumatology International Trials Organisation/American College of Rheumatology/European League Against Rheumatism Disease activity core set for the evaluation of response to therapy in juvenile dermatomyositis: a prospective vaNicolino Ruperto
IRCCS G Gaslini, Genoa, Italy
Arthritis Rheum 59:4-13. 2008..To validate a core set of outcome measures for the evaluation of response to treatment in patients with juvenile dermatomyositis (DM)...
Outcome in juvenile onset systemic lupus erythematosusAngelo Ravelli
Dipartimento di Pediatria, Universita di Genova, Unita Operativa Pediatria II, Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Italy
Curr Opin Rheumatol 17:568-73. 2005..This review summarizes the recent advances in the investigation on survival, accumulated damage, and health-related quality of life in patients with juvenile-onset systemic lupus erythematosus...
Treatment of autoinflammatory syndromesMarco Gattorno
UO Pediatria II, G Gaslini Institute, Genova, Italy
Curr Opin Pediatr 22:771-8. 2010..In this review, we outline the more recent novelties in the treatment of autoinflammatory diseases and their possible implications for some multifactorial pediatric conditions...
Antiphospholipid syndromeAngelo Ravelli
Pediatria II, Istituto di Ricovero e Cura a Carattere Scientifico G Gaslini, Largo G Gaslini, 5, 16147, Genoa, Italy
Pediatr Clin North Am 52:469-91, vi. 2005....
Current medical treatments for juvenile idiopathic arthritisNicolino Ruperto
Pediatria II e Reumatologia, Istituto G Gaslini Genoa, University of Genoa Genoa, Italy
Front Pharmacol 2:60. 2011..This review will currently describe the methodological approach for performing clinical trials in JIA as well as the current available drug treatment...
Phenotypic and functional characterisation of CCR7+ and CCR7- CD4+ memory T cells homing to the joints in juvenile idiopathic arthritisMarco Gattorno
II Division of Pediatrics, University of Genoa, Genoa, Italy
Arthritis Res Ther 7:R256-67. 2005..Moreover, discrete patterns of chemokine receptor expression are detected in the synovial tissue...
International research networks in pediatric rheumatology: the PRINTO perspectiveNicolino Ruperto
IRCCS G Gaslini, Universita di Genova, Pediatria II Reumatologia, Genova, Italy
Curr Opin Rheumatol 16:566-70. 2004..The purpose of this review is to highlight the problems and possible solutions for the conduct of international collaborative research for pediatric rheumatic diseases...
A randomized, double-blind clinical trial of two doses of meloxicam compared with naproxen in children with juvenile idiopathic arthritis: short- and long-term efficacy and safety resultsNicolino Ruperto
IRCCS G Gaslini, Pediatria II, Reumatologia, Genoa, Italy
Arthritis Rheum 52:563-72. 2005....
Patients with antinuclear antibody-positive juvenile idiopathic arthritis constitute a homogeneous subgroup irrespective of the course of joint diseaseAngelo Ravelli
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Arthritis Rheum 52:826-32. 2005....
A randomized trial of parenteral methotrexate comparing an intermediate dose with a higher dose in children with juvenile idiopathic arthritis who failed to respond to standard doses of methotrexateNicolino Ruperto
IRCCS G Gaslini, University of Genoa, Genoa, Italy
Arthritis Rheum 50:2191-201. 2004..5 mg/m(2)/week)...
