Research Topics
Genomes and Genes
| Rachele CaglianiSummaryAffiliation: Bosisio Parini Country: Italy Publications
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Detail Information
Publications
A CAV3 microdeletion differentially affects skeletal muscle and myocardiumR Cagliani
I R C C S E Medea, Bosisio Parini, Italy
Neurology 61:1513-9. 2003....
Molecular analysis of LGMD-2B and MM patients: identification of novel DYSF mutations and possible founder effect in the Italian populationR Cagliani
IRCCS E Medea, Associazione La Nostra Famiglia, Via Don Luigi Monza 20, 23842 Bosisio Parini LC, Italy
Neuromuscul Disord 13:788-95. 2003..The possible existence of a founder effect for the Arg959Trp mutation in the Italian population is discussed...
An intragenic deletion/inversion event in the DMD gene determines a novel exon creation and results in a BMD phenotypeRachele Cagliani
I R C C S E Medea, Associazione La Nostra Famiglia, Via Don Luigi Monza 20, 23842, Bosisio Parini LC, Italy
Hum Genet 115:13-8. 2004..This case might provide further insight into both the mechanisms that determine genomic rearrangements in the DMD locus and the molecular signals that drive exon inclusion...
Population genetics of IFIH1: ancient population structure, local selection, and implications for susceptibility to type 1 diabetesMatteo Fumagalli
Bioinformatic Lab, Scientific Institute Istituto di Ricovero e Cura a Carattere Scientifico E Medea, Bosisio Parini, Lecco, Italy
Mol Biol Evol 27:2555-66. 2010....
A positively selected APOBEC3H haplotype is associated with natural resistance to HIV-1 infectionRachele Cagliani
Scientific Institute IRCCS E Medea, via Don L Monza 20, Bosisio Parini LC, Italy
Evolution 65:3311-22. 2011..Our data represent an example of how the selective pressures exerted by extinct or unknown viral agents can be exploited to provide valuable information on the allelic determinants of susceptibility to modern infections...
Polymorphisms in the CPB2 gene are maintained by balancing selection and result in haplotype-preferential splicing of exon 7Rachele Cagliani
Bioinformatic Laboratory, Scientific Institute IRCCS E Medea, Bosisio Parini LC, Italy
Mol Biol Evol 27:1945-54. 2010..These data highlight the contribution of population genetics approaches to the analysis of functional genetic variation and may orient further biochemical and genetics studies on the pathophysiologic role of CPB2 gene products...
A complex selection signature at the human AVPR1B geneRachele Cagliani
Scientific Institute IRCCS E, Medea, Bioinformatic Lab, Bosisio Parini, LC, Italy
BMC Evol Biol 9:123. 2009....
Identification of a new susceptibility variant for multiple sclerosis in OAS1 by population genetics analysisRachele Cagliani
Bioinformatic Lab, Scientific Institute IRCCS E Medea, via Don L Monza 20, 23842, Bosisio Parini, LC, Italy
Hum Genet 131:87-97. 2012....
Over-representation of exonic splicing enhancers in human intronless genes suggests multiple functions in mRNA processingUberto Pozzoli
Scientific Institute IRCCS E Medea, Associazione La Nostra Famiglia, 23842 Bosisio Parini LC, Italy
Biochem Biophys Res Commun 322:470-6. 2004..These observations suggest that SR proteins (and possibly other splicing factors) play a role in cellular processes distinct from splicing...
The signature of long-standing balancing selection at the human defensin beta-1 promoterRachele Cagliani
Scientific Institute IRCCS E, Medea, Bioinformatic Lab, Bosisio Parini LC, Italy
Genome Biol 9:R143. 2008....
Relevance of sequence and structure elements for deletion events in the dystrophin gene major hot-spotManuela Sironi
IRCCS E Medea, Associazione La Nostra Famiglia, Via Don Luigi Monza 20, 23842, Bosisio Parini LC, Italy
Hum Genet 112:272-88. 2003..This study highlights the importance of a whole gene approach to rule out the presumptive role of specific features that, when locally analyzed, might suggest involvement in gene rearrangements...
Silencer elements as possible inhibitors of pseudoexon splicingManuela Sironi
IRCCS E Medea, Associazione La Nostra Famiglia, 23842 Bosisio Parini, LC, Italy
Nucleic Acids Res 32:1783-91. 2004....
Widespread balancing selection and pathogen-driven selection at blood group antigen genesMatteo Fumagalli
Scientific Institute IRCCS E Medea, Bioinformatic Lab, 23842 Bosisio Parini LC, Italy
Genome Res 19:199-212. 2009....
Genetic variability in the ACE gene region surrounding the Alu I/D polymorphism is maintained by balancing selection in human populationsRachele Cagliani
Scientific Institute IRCCS E Medea, Bioinformatic Laboratory, Bosisio Parini LC, Italy
Pharmacogenet Genomics 20:131-4. 2010..The aim of our study was to verify whether the Alu insertion/deletion (Alu I/D) polymorphism or any linked variant has been maintained by natural selection in human populations...
Genetic diversity at endoplasmic reticulum aminopeptidases is maintained by balancing selection and is associated with natural resistance to HIV-1 infectionRachele Cagliani
Bioinformatic Laboratory, Scientific Institute IRCCS E Medea, via Don L Monza 20, Bosisio Parini LC, Italy
Hum Mol Genet 19:4705-14. 2010....
Comparative analysis of vertebrate dystrophin loci indicate intron gigantism as a common featureUberto Pozzoli
IRCCS E Medea, Associazione La Nostra Famiglia, 23842 Bosisio Parini LC, Italy
Genome Res 13:764-72. 2003..The hypothesis that intron length might be functionally relevant to the DMD gene regulation is proposed and substantiated by the finding that dystrophin intron gigantism is common to the three vertebrate genes...
Intron size in mammals: complexity comes to terms with economyUberto Pozzoli
Bioinformatic Laboratory, Scientific Institute IRCCS E Medea, via Don L Monza 20, 23842 Bosisio Parini LC, Italy
Trends Genet 23:20-4. 2007....
Genome-wide identification of susceptibility alleles for viral infections through a population genetics approachMatteo Fumagalli
Scientific Institute IRCCS E Medea, Bioinformatic Lab, Bosisio Parini LC, Italy
PLoS Genet 6:e1000849. 2010....
Mutation finding in patients with dysferlin deficiency and role of the dysferlin interacting proteins annexin A1 and A2 in muscular dystrophiesRachele Cagliani
IRCCS E Medea, Associazione La Nostra Famiglia, Bosisio Parini, Lecco, Italy
Hum Mutat 26:283. 2005..The positive correlation between annexin A1 and A2 and clinical severity, as well as muscle histopathology, suggests that their level may be a prognostic indicator of disease...
The role of protozoa-driven selection in shaping human genetic variabilityUberto Pozzoli
Scientific Institute IRCCS E Medea, Bioinformatic Laboratory, via Don L Monza 20, 23842 Bosisio Parini LC, Italy
Trends Genet 26:95-9. 2010..We provide a genome-wide estimate of protozoa-driven selective pressure and identify candidate susceptibility genes for protozoa-borne diseases...
Both selective and neutral processes drive GC content evolution in the human genomeUberto Pozzoli
Scientific Institute IRCCS E, Medea, Bioinformatic Lab, Via don L, Monza 20, 23842 Bosisio Parini LC, Italy
BMC Evol Biol 8:99. 2008..Mammalian genomes consist of regions differing in GC content, referred to as isochores or GC-content domains. The scientific debate is still open as to whether such compositional heterogeneity is a selected or neutral trait...
Fixation of conserved sequences shapes human intron size and influences transposon-insertion dynamicsManuela Sironi
Scientific Institute IRCCS E, Medea, Via Don Luigi Monza 20, 23842 Bosisio Parini (LC, Italy
Trends Genet 21:484-8. 2005..Analysis of TE and MCS distribution suggested an unprecedented estimate of information requirements for proper splicing of long introns with indication of sequence constraints extending up to >3 kb downstream 5' splice sites...
Genetic variability at the TREX1 locus is not associated with natural resistance to HIV-1 infectionManuela Sironi
Scientific Institute IRCCS E Medea, Bosisio Parini, Lecco, Italy
AIDS 26:1443-5. 2012....
Variants in SNAP25 are targets of natural selection and influence verbal performances in womenRachele Cagliani
Bioinformatic Lab, Scientific Institute IRCCS E Medea, via Don L Monza 20, Bosisio Parini, LC, Italy
Cell Mol Life Sci 69:1705-15. 2012..Although caution should be used in inferring selective pressures from observed signatures, SNAP25 might represent the first description of an adaptively evolving gene with a role in cognition...
An evolutionary analysis of RAC2 identifies haplotypes associated with human autoimmune diseasesManuela Sironi
Bioinformatics Laboratory, Scientific Institute IRCCS E Medea, Bosisio Parini LC, Italy
Mol Biol Evol 28:3319-29. 2011..Other genes with a role in RICD have previously been associated with autoimmunity in humans, suggesting that this pathway and RAC2 may represent novel therapeutic targets in autoimmune disorders...
Comparative analysis of the human dystrophin and utrophin gene structuresUberto Pozzoli
IRCCS E Medea, Associazione La Nostra Famiglia, 23842 Bosisio Parini, LC, Italy
Genetics 160:793-8. 2002..Out-of-frame rod-domain exons have stronger splice sites and are separated by significantly longer introns as compared to in-frame exons. These features are unique for the two homologs and not shared by other spectrin superfamily genes...
Congenital muscular dystrophy with muscle inflammation alpha dystroglycan glycosylation defect and no mutation in FKRP geneCostanza Lamperti
Centro Dino Ferrari, Dipartimento di Scienze Neurologiche, Unita' Operativa Neurologia, Fondazione I.R.C.C.S. Ospedale Maggiore Policlinico- Mangiagalli e Regina Elena, University of Milan, Milan, Italy
J Neurol Sci 243:47-51. 2006..The analysis of FKRP, LARGE, POMT1 and POMGnT1 genes did not show any pathogenic mutations, suggesting that at least another gene may account for CMD with secondary glycosylated alpha-DG deficiency...
Clinical, molecular, and protein correlations in a large sample of genetically diagnosed Italian limb girdle muscular dystrophy patientsMichela Guglieri
Centro Dino Ferrari, Dipartimento di Scienze Neurologiche, Universita degli Studi di Milano, Milano, Italy
Hum Mutat 29:258-66. 2008..1 years vs. 36.7+/-11.1 years; P=0.0037). Similarly, dysferlin absence was associated with an earlier onset when compared to partial deficiency (20.2+/-standard deviation [SD] 5.2 years vs. 28.4+/-SD 11.2 years; P=0.014)...
Gene function and expression level influence the insertion/fixation dynamics of distinct transposon families in mammalian intronsManuela Sironi
Scientific Institute IRCCS E Medea, Bioinformatic Lab, Via don L Monza, 23842 Bosisio Parini (LC, Italy
Genome Biol 7:R120. 2006..Moreover, we provide the first report showing that a specific TE family is evolutionarily associated with a gene function category...
Analysis of intronic conserved elements indicates that functional complexity might represent a major source of negative selection on non-coding sequencesManuela Sironi
Scientific Institute IRCCS E. Medea, 23842 Bosisio Parini (LC, Italy
Hum Mol Genet 14:2533-46. 2005....
Calpain 3 deficiency in Quail Eater's diseaseOlimpia Musumeci
Ann Neurol 55:146-7. 2004
