Research Topics
Species | Gudrun A RappoldSummaryAffiliation: University of Heidelberg Country: Germany Publications
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Detail Information
Publications
Complex evolution of a Y-chromosomal double homeobox 4 (DUX4)-related gene family in hominoidsJulia Schmidt
Institute of Human Genetics, University of Freiburg, Freiburg, Germany
PLoS ONE 4:e5288. 2009....
Mutational analysis of the PITX2 coding region revealed no common cause for transposition of the great arteries (dTGA)Nadja Muncke
Institut fur Humangenetik, Universitat Heidelberg, INF 366, 69120 Heidelberg, Germany
BMC Med Genet 6:20. 2005..TGA accounts for 5-7% of all congenital heart diseases affecting 0.2 per 1000 live births, thereby representing the most frequent cyanotic heart defect diagnosed in the neonatal period...
Deletions of the homeobox gene SHOX (short stature homeobox) are an important cause of growth failure in children with short statureGudrun A Rappold
Institute of Human Genetics, University of Heidelberg, 69120 Heidelberg, Germany
J Clin Endocrinol Metab 87:1402-6. 2002....
Cloning, physical mapping and expression analysis of the human 5-HT3 serotonin receptor-like genes HTR3C, HTR3D and HTR3EBeate Niesler
Institute of Human Genetics, University of Heidelberg, Im Neuenheimer Feld 328, 69120, Heidelberg, Germany
Gene 310:101-11. 2003....
The short stature homeodomain protein SHOX induces cellular growth arrest and apoptosis and is expressed in human growth plate chondrocytesAntonio Marchini
Institute of Human Genetics, University of Heidelberg, Im Neuenheimer Feld 328, D 69120 Heidelberg, Germany
J Biol Chem 279:37103-14. 2004..This study provides the first insight into the biological function of SHOX as regulator of cellular proliferation and viability and relates these cellular events to the phenotypic consequences of SHOX deficiency...
Transcriptional and translational regulation of the Leri-Weill and Turner syndrome homeobox gene SHOXRudiger J Blaschke
Institute of Human Genetics, Ruprecht Karls University, Im Neuenheimer Feld 328, 69120 Heidelberg, Germany
J Biol Chem 278:47820-6. 2003..In conclusion, our data support a model where functional SHOX protein levels are regulated by a combination of transcriptional and translational control mechanisms...
The definition of the Y chromosome growth-control gene (GCY) critical region: relevance of terminal and interstitial deletionsStefan Kirsch
Institute of Human Genetics, University of Heidelberg, Heidelberg, Germany
J Pediatr Endocrinol Metab 15:1295-300. 2002..No functional gene has been identified in this region...
The distinct and overlapping phenotypic spectra of FOXP1 and FOXP2 in cognitive disordersClaire Bacon
Department of Human Molecular Genetics, University of Heidelberg, Im Neuenheimer Feld 366, 69120 Heidelberg, Germany
Hum Genet 131:1687-98. 2012....
The human SHOX mutation databaseBeate Niesler
Institute of Human Genetics, University of Heidelberg, Heidelberg, Germany
Hum Mutat 20:338-41. 2002..2002]. The database is accessible via the website www.shox.uni-hd.de. It contains general information about the SHOX gene, and allows remote users to search the data and to submit new mutations to the database...
The novel Rho-GTPase activating gene MEGAP/ srGAP3 has a putative role in severe mental retardationVolker Endris
Institut fur Humangenetik, Universitat Heidelberg, Im Neuenheimer Feld 328, 69120 Heidelberg, Germany
Proc Natl Acad Sci U S A 99:11754-9. 2002..We propose that haploinsufficiency of MEGAP/srGAP3 leads to the abnormal development of neuronal structures that are important for normal cognitive function...
All shook up by SHOX deficiencyGudrun A Rappold
J Pediatr 147:422-4. 2005
Pseudoautosomal linkage of familial Hodgkin's lymphoma: molecular analysis of a unique family with Leri-Weill dyschondrosteosis and Hodgkins lymphomaDeborah J Shears
Br J Haematol 121:377-9. 2003
Congenital conductive hearing loss in dyschondrosteosisEls M R De Leenheer
Department of Otorhinolaryngology, University Medical Center St Radboud, Nijmegen, The Netherlands
Ann Otol Rhinol Laryngol 112:153-8. 2003..In our patient, exploratory tympanotomy revealed ankylosis of the stapes and a malformed incus. A substantial gain in hearing threshold was obtained by a stapedectomy in combination with a malleovestibulopexy...
Molecular characterization of a ring X chromosome in a male with short statureJay W Ellison
Department of Medical Genetics, Mayo Clinic, 200 First St SW, Rochester, MN 55905, USA
Hum Genet 110:322-6. 2002..The findings are also relevant to observations made of "complete" ring chromosomes...
Direct evidence for the Homo-Pan cladeRainer Wimmer
Institute of Human Genetics and Anthropology, University of Freiburg, Germany
Chromosome Res 10:55-61. 2002..Thus, this shared derived (synapomorphic) trait provides clear evidence for a Homo-Pan clade independent of DNA sequence analysis...
