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Genomes and Genes | Gerald SimonneauSummaryCountry: France Publications
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Publications
A randomized study comparing the efficacy and safety of nadroparin 2850 IU (0.3 mL) vs. enoxaparin 4000 IU (40 mg) in the prevention of venous thromboembolism after colorectal surgery for cancerG Simonneau
Department of Pulmonary and Critical Medicine, Antoine Beclere University Hospital, Clamart, France
J Thromb Haemost 4:1693-700. 2006..The optimal thromboprophylactic dosage regimen of low-molecular-weight heparins in high-risk general surgery remains debatable...
Selexipag: an oral, selective prostacyclin receptor agonist for the treatment of pulmonary arterial hypertensionGerald Simonneau
National Reference Center for Pulmonary Hypertension South Paris University, Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, 92141 Clamart Cedex, France
Eur Respir J 40:874-80. 2012..Selexipag was well tolerated with a safety profile in line with the expected pharmacological effect. Our results encourage the further investigation of selexipag for the treatment of PAH...
A hemodynamic study of pulmonary hypertension in sickle cell diseaseFlorence Parent
Universite Paris Sud, Kremlin Bicetre, Hopital Antoine Beclere, Clamart, France
N Engl J Med 365:44-53. 2011..The prevalence and characteristics of pulmonary hypertension in adults with sickle cell disease have not been clearly established...
[A new clinical classification of pulmonary hypertension]Gerald Simonneau
Universite Paris Sud 11, UPRES EA 2705, Centre National de Référence de l Hypertension Artérielle Pulmonaire, Pneumologie et Réanimation respiratoire, Hopital Antoine Beclere, 157, rue de la Porte de Trivaux 92141 Clermont cedex, France
Bull Acad Natl Med 193:1897-909. 2009....
Updated clinical classification of pulmonary hypertensionGerald Simonneau
Centre National de Référence des Maladies Vasculaires Pulmonaires, Universite Paris Sud, Hopital Antoine Beclere, Clamart, France
J Am Coll Cardiol 54:S43-54. 2009..Finally, it was decided to place pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis in a separate group, distinct from but very close to Group 1 (now called Group 1'). Thus, Group 1 of PAH is now more homogeneous...
Long-term outcome of systemic sclerosis-associated pulmonary arterial hypertension treated with bosentan as first-line monotherapy followed or not by the addition of prostanoids or sildenafilDavid Launay
Universite Paris Sud, Faculte de Medecine, Kremlin Bice tre, France
Rheumatology (Oxford) 49:490-500. 2010..We aimed to describe the long-term outcome of SSc-PAH treated with first-line monotherapy bosentan followed or not by the addition of prostanoids or sildenafil...
Absence of influence of gender and BMPR2 mutation type on clinical phenotypes of pulmonary arterial hypertensionBarbara Girerd
Faculte de Medecine, Universite Paris Sud, Kremlin Bicetre, F 94276, France
Respir Res 11:73. 2010..A recent report has suggested that this may only be the case for females and that patients with missense mutations in BMPR2 gene have more severe disease than patients with truncating mutations...
Characterization of pulmonary arterial hypertension patients walking more than 450 m in 6 min at diagnosisBruno Degano
Service de Pneumologie, Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, 92141 Clamart, France
Chest 137:1297-303. 2010..Because they are generally excluded from randomized controlled trials, little is known about these patients...
[Pulmonary arterial hypertension]Xavier Jais
Centre de référence de l hypertension pulmonaire sévère, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, 92141 Clamart Cedex, France
Rev Prat 58:1997-2010. 2008..The evolution of therapy from vasodilators to antiproliferative agents reflects the advancement in our understanding of the mechanisms mediating pulmonary arterial hypertension...
Clinical outcomes of pulmonary arterial hypertension in patients carrying an ACVRL1 (ALK1) mutationBarbara Girerd
Universite Paris Sud, Faculte de Medecine, Kremlin Bicetre, 92140 Clamart, France
Am J Respir Crit Care Med 181:851-61. 2010..Activin A receptor type II-like kinase-1 (ACVRL1, also known as ALK1) mutation is a cause of hereditary hemorrhagic telangiectasia (HHT) and/or heritable pulmonary arterial hypertension (PAH)...
HIV-associated pulmonary arterial hypertension: survival and prognostic factors in the modern therapeutic eraBruno Degano
Centre National de Référence de l Hypertension Artérielle Pulmonaire, Service de Pneumologie, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud 11, Clamart, France
AIDS 24:67-75. 2010....
Survival in patients with idiopathic, familial, and anorexigen-associated pulmonary arterial hypertension in the modern management eraMarc Humbert
Service de Pneumologie et Reanimation Respiratoire, Faculte de Medecine, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud 11, 92140 Clamart, France
Circulation 122:156-63. 2010..We conducted a study to characterize mortality in a multicenter prospective cohort of patients diagnosed with idiopathic, familial, or anorexigen-associated pulmonary arterial hypertension in the modern management era...
Pulmonary veno-occlusive disease: recent progress and current challengesDavid Montani
Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud 11, INSERM U999, Centre National de Référence de l Hypertension Pulmonaire Sévère, 92140 Clamart, France
Respir Med 104:S23-32. 2010..Unfortunately, the long term effects of these agents are variable and lung transplantation remains the treatment of choice...
Bosentan for treatment of inoperable chronic thromboembolic pulmonary hypertension: BENEFiT (Bosentan Effects in iNopErable Forms of chronIc Thromboembolic pulmonary hypertension), a randomized, placebo-controlled trialXavier Jais
Antoine Beclere Hospital, Clamart, France
J Am Coll Cardiol 52:2127-34. 2008..Our goal was to investigate the effect of treatment with the oral dual endothelin receptor antagonist bosentan on the hemodynamics and exercise capacity of patients with chronic thromboembolic pulmonary hypertension (CTEPH)...
Portopulmonary hypertension: survival and prognostic factorsJerome Le Pavec
Universite Paris Sud 11, UPRES 2705, Service de Pneumologie, Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, 92140 Clamart, France
Am J Respir Crit Care Med 178:637-43. 2008..Survival results in PoPH are contrasting, and prognostic factors need to be identified...
Endothelin receptor antagonists for the treatment of pulmonary arterial hypertensionDermot S O'Callaghan
Universite Paris Sud, Faculte de Medecine, Le Kremlin Bicetre, F 94276, France
Expert Opin Pharmacother 12:1585-96. 2011..This is of crucial importance to ensure that future developments are both worthwhile and acceptable to patients, physicians, health system payers and regulatory authorities...
Evidence for the use of combination targeted therapeutic approaches for the management of pulmonary arterial hypertensionDermot S O'Callaghan
Universite Paris Sud, Faculte de Medecine, Kremlin Bicêtre F 94276, France
Respir Med 104:S74-80. 2010..This review details the rationale for the different combination strategies and examines the clinical evidence in favour of some of the approaches that have been evaluated...
Addition of sildenafil to long-term intravenous epoprostenol therapy in patients with pulmonary arterial hypertension: a randomized trialGerald Simonneau
Service de Pneumologie, Hopital Antoine Beclere, Universite Paris Sud, Clamart, France
Ann Intern Med 149:521-30. 2008..Oral sildenafil and intravenous epoprostenol have independently been shown to be effective in patients with pulmonary arterial hypertension...
Phosphodiesterase type 5 inhibitors in pulmonary arterial hypertensionDavid Montani
Universite Paris Sud, Orsay, France
Adv Ther 26:813-25. 2009..Due to their clinical effectiveness, tolerance profile, and their oral administration, sildenafil and tadalafil are two of the recommended first-line therapies for PAH patients in World Health Organization functional classes II or III...
Intravenous epoprostenol in inoperable chronic thromboembolic pulmonary hypertensionSégolène Cabrol
Centre des Maladies Vasculaires Pulmonaires UPRES EA 2705, Service de Pneumologie et Reanimation, AP HP, Universite Paris Sud, Hopital Antoine Beclere, Clamart, France
J Heart Lung Transplant 26:357-62. 2007..Vascular remodeling lesions can be found in lungs of patients with CTEPH. Little is known about epoprostenol therapy in inoperable distal CTEPH patients...
Long-term response to calcium channel blockers in idiopathic pulmonary arterial hypertensionOlivier Sitbon
Centre des Maladies Vasculaires Pulmonaires, UPRES EA 2705, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, AP HP, Universite Paris Sud, Clamart, France
Circulation 111:3105-11. 2005..Characteristics of patients with idiopathic pulmonary arterial hypertension (IPAH) who benefit from long-term calcium channel blockers (CCB) are unknown...
Usefulness of first-line combination therapy with epoprostenol and bosentan in pulmonary arterial hypertension: an observational studyKristina Kemp
Universite Paris Sud 11, Faculte de Medecine, Le Kremlin Bicetre, Clamart, France
J Heart Lung Transplant 31:150-8. 2012..Recent guidelines have proposed first-line combination therapy as a potential strategy for the treatment of functional class IV pulmonary arterial hypertension (PAH)...
Immunosuppressive therapy in lupus- and mixed connective tissue disease-associated pulmonary arterial hypertension: a retrospective analysis of twenty-three casesXavier Jais
Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud, Clamart, France
Arthritis Rheum 58:521-31. 2008..To describe the response to first-line immunosuppressive therapy with or without pulmonary vasodilators in pulmonary arterial hypertension (PAH) associated with systemic lupus erythematosus (SLE) or mixed connective tissue disease (MCTD)...
Pulmonary veno-occlusive disease: clinical, functional, radiologic, and hemodynamic characteristics and outcome of 24 cases confirmed by histologyDavid Montani
Universite Paris Sud 11, UPRES EA 2705, Centre des Maladies Vasculaires Pulmonaires, Paris, France
Medicine (Baltimore) 87:220-33. 2008..Clinical outcomes of PVOD patients were worse than those of PAH patients...
[Pulmonary arterial hypertension associated with common diseases: connective-tissue diseases, HIV infection and portal hypertension]Olivier Sitbon
Centre de référence national de l HTAP, Service de Pneumologie, UPRES EA2705, Hopital Antoine Beclere, AP HP, Université Paris XI Sud, 92141 Clamart Cedex, France
Rev Prat 58:2011-8. 2008..However, their prognosis differs greatly: it is poor in scleroderma, and much better in congenital heart diseases...
[Pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis]David Montani
Univ Paris Sud, Faculte de Medecine, Kremlin Bicetre, F 94276, France
Presse Med 39:134-43. 2010..In patients with the most severe disease, the prudent use of continuous intravenous epoprostenol, can serve as bridge-therapy while awaiting a lung transplant...
Screening for pulmonary arterial hypertension in patients with systemic sclerosis: clinical characteristics at diagnosis and long-term survivalMarc Humbert
Universite Paris Sud, Le Kremlin Bicetre, France AP HP Hôpital Antoine Béclère, Clamart, France
Arthritis Rheum 63:3522-30. 2011..However, little is known about the impact of detection programs on patients with SSc-PAH. This study was undertaken to assess the clinical characteristics of patients with SSc-PAH at diagnosis and their long-term outcomes...
Effects of the dual endothelin receptor antagonist bosentan in patients with pulmonary arterial hypertension: a 1-year follow-up studyOlivier Sitbon
Service de Pneumologie Réanimation Respiratoire, Hopital Antoine Beclere, 157, Avenue de la Porte Trivaux, F 92141 Clamart Cedex, France
Chest 124:247-54. 2003..We report on the long-term safety and efficacy of bosentan treatment in patients with pulmonary arterial hypertension (PAH)...
Clinical outcomes of pulmonary arterial hypertension in carriers of BMPR2 mutationBenjamin Sztrymf
Universite Paris Sud 11, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, 92140 Clamart, France
Am J Respir Crit Care Med 177:1377-83. 2008..Germline mutations in the gene encoding for bone morphogenetic protein receptor 2 (BMPR2) are a cause of pulmonary arterial hypertension (PAH)...
Chemokine RANTES in severe pulmonary arterial hypertensionPeter Dorfmuller
Center for Pulmonary Vascular Diseases, UPRES EA 2705, France
Am J Respir Crit Care Med 165:534-9. 2002..These results support the concept that inflammatory mechanisms play a role in the natural history of pulmonary arterial hypertension...
Therapeutic advances in pulmonary arterial hypertensionK Boutet
Universite Paris Sud 11, Centre des Maladies Vasculaires Pulmonaires, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Clamart, France
Ther Adv Respir Dis 2:249-65. 2008..Despite those important advances there is still no cure for PAH. Fortunately, research is ongoing and many drugs show promises...
Idiopathic pulmonary arterial hypertension and pulmonary veno-occlusive disease: similarities and differencesDavid Montani
Universite Paris Sud 11, Centre National de Référence de l Hypertension Artérielle Pulmonaire, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Clamart, France
Semin Respir Crit Care Med 30:411-20. 2009..Lung transplantation remains the treatment of choice, but cautious use of specific PAH therapy can be helpful in select patients while awaiting this intervention...
Pulmonary arterial hypertension in France: results from a national registryMarc Humbert
UPRES EA 2705, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud, 157 rue de la Porte de Trivaux, 92140 Clamart, France
Am J Respir Crit Care Med 173:1023-30. 2006..Pulmonary arterial hypertension (PAH) is an orphan disease for which the trend is for management in designated centers with multidisciplinary teams working in a shared-care approach...
An extreme consequence of splenectomy in dehydrated hereditary stomatocytosis: gradual thrombo-embolic pulmonary hypertension and lung-heart transplantationXavier Jais
UPRES EA 2705, Service de Pneumologie, Hopital Antoine Béclere AP HP, Universite Paris Sud, Clamart, France
Hemoglobin 27:139-47. 2003..This case ranks as one of the most severe examples ever recorded of the effect that splenectomy may have in DHS patients. Nonetheless, it represents the first case to receive a heart-lung transplant...
Pulmonary arterial hypertension in a patient with Cowden syndrome and anorexigen exposureDelphine Natali
Faculte de Medecine, Universite Paris Sud, Kremlin Bicetre, France
Chest 140:1066-8. 2011..In this case report, we hypothesize that PTEN mutations may be a predisposing factor for the development of PAH, with anorexigen exposure as a potential trigger...
The CX3C chemokine fractalkine in allergic asthma and rhinitisAnne Cécile Rimaniol
Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Universite Paris Sud, Clamart, France
J Allergy Clin Immunol 112:1139-46. 2003..Because of its dual activity, fractalkine plays a major role in the transendothelial and transepithelial migration of leukocytes during inflammation...
Treatment of pulmonary arterial hypertension with targeted therapiesDermot S O'Callaghan
Universite Paris Sud, Faculte de Medecine, Le Kremlin Bicêtre F 94276, France
Nat Rev Cardiol 8:526-38. 2011..In this Review, we highlight the pharmacological agents currently available for the treatment of PAH and discuss potential novel strategies...
Platelet-derived growth factor expression and function in idiopathic pulmonary arterial hypertensionFrederic Perros
Centre National de Référence de l Hypertension Artérielle Pulmonaire, Service de Pneumologie et Reanimation Respiratoire, Institut Paris Sud Cytokines, Hopital Antoine Beclere, Universite Paris Sud 11, UPRES EA 2705, Clamart, France
Am J Respir Crit Care Med 178:81-8. 2008....
Efficacy, safety and pharmacokinetics of bosentan in portopulmonary hypertensionLaurent Savale
Faculte de Medecine, Universite Paris Sud 11, France
Eur Respir J 41:96-103. 2013..Haemodynamic improvements were particularly pronounced in patients with more severe cirrhosis. The safety profile of bosentan was consistent with previous studies...
Idiopathic pulmonary hypertension: what did we learn from genes?Benjamin Sztrymf
UPRES 2705, Service de Pneumologie et Reanimation Respiratoire, Centre des Maladies Vasculaires Pulmonaires, Hopital Antoine Beclere, Universite Paris Sud, Clamart, France
Sarcoidosis Vasc Diffuse Lung Dis 22:S91-100. 2005..Nevertheless, PAH pathobiology remains unclear and genomic approaches may identify additional molecular determinants for this disorder...
Pulmonary arterial hypertension and HIV infectionBruno Degano
Service de Pneumologie, Hopital Antoine Beclere, 92141 Clamart, France
Semin Respir Crit Care Med 30:440-7. 2009..Other PAH therapies, including prostacyclin analogs, type 5 phosphodiesterase inhibitors, and single endothelin receptor antagonists, have yet to be evaluated in PAH-HIV...
Prevalence of HIV-related pulmonary arterial hypertension in the current antiretroviral therapy eraOlivier Sitbon
Service de Pneumologie Hôpital Antoine Béclère, 157 rue de la Porte de Trivaux, 92141 Clamart, France
Am J Respir Crit Care Med 177:108-13. 2008..The prevalence of HIV-associated pulmonary arterial hypertension (PAH) has not been evaluated since introduction of combined, highly active antiretroviral treatments...
Increased oxidative stress and severe arterial remodeling induced by permanent high-flow challenge in experimental pulmonary hypertensionPeter Dorfmuller
Universite Paris Sud, Faculte de Medecine, Kremlin Bicetre, F 94276, France
Respir Res 12:119. 2011..The impact of OS on vascular remodeling in PH is still to be determined. We hypothesized, that augmented blood-flow could increase OS and might thereby contribute to DC/inflammatory cell-recruitment and smooth-muscle-cell-proliferation...
Pulmonary arterial hypertension: a rare complication of primary Sjögren syndrome: report of 9 new cases and review of the literatureDavid Launay
Centre National de Référence de l Hypertension Artérielle Pulmonaire, UPRES EA2705, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud 11, Clamart, France
Medicine (Baltimore) 86:299-315. 2007..In conclusion, this report underlines the rarity and severity of PAH in pSS patients. The best therapeutic regimen remains to be defined but should include standard PAH therapy and/or immunosuppressants...
Long-term intravenous epoprostenol infusion in primary pulmonary hypertension: prognostic factors and survivalOlivier Sitbon
Service de Pneumologie et Reanimation, UPRES EA 2705 on Pulmonary Vascular Diseases, Hopital Antoine Beclere, Universite Paris Sud, Clamart, France
J Am Coll Cardiol 40:780-8. 2002..We sought to determine the factors associated with long-term survival in patients with primary pulmonary hypertension (PPH) treated with continuous epoprostenol infusion...
Deleterious effects of beta-blockers on exercise capacity and hemodynamics in patients with portopulmonary hypertensionSteeve Provencher
Centre des Maladies Vasculaires Pulmonaires UPRES EA 2705, Service de Pneumologie, Hopital Antoine Beclere, Clamart, France
Gastroenterology 130:120-6. 2006..The aim of this study was to investigate the effect of beta-blockers on exercise capacity and pulmonary hemodynamics in patients with portopulmonary hypertension receiving beta-blockers for the prophylaxis of variceal bleeding...
Pulmonary veno-occlusive disease: the bête noire of pulmonary hypertension in connective tissue diseases?Dermot S O'Callaghan
Faculte de Medecine, Universite Paris Sud, 94276 Kremlin Bicêtre, France
Presse Med 40:e65-78. 2011..This review summarises the epidemiologic, clinico-pathologic and imaging characteristics of PVOD in the setting of CTD and discusses potential management approaches...
Bosentan for the treatment of human immunodeficiency virus-associated pulmonary arterial hypertensionOlivier Sitbon
Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, 92140 Clamart, France
Am J Respir Crit Care Med 170:1212-7. 2004....
Ventilation/perfusion lung scan in pulmonary veno-occlusive diseaseAndrei Seferian
Universite Paris Sud, Faculte de Medecine, Le Kremlin Bicetre, France
Eur Respir J 40:75-83. 2012..Future recommendations should be amended according to these results suggesting that V'/Q' lung scanning is not useful in discriminating PVOD from idiopathic PAH...
C-kit-positive cells accumulate in remodeled vessels of idiopathic pulmonary arterial hypertensionDavid Montani
University Paris Sud, Faculte de Medecine, Kremlin Bicetre, France
Am J Respir Crit Care Med 184:116-23. 2011..Because recent studies suggest that c-kit may be a target for innovative therapies in experimental pulmonary hypertension, we investigated the contribution of c-kit(+) cells in human idiopathic pulmonary arterial hypertension (IPAH)...
Rapid switch from intravenous epoprostenol to intravenous treprostinil in patients with pulmonary arterial hypertensionOlivier Sitbon
Service de Pneumologie, Hopital Antoine Beclere, Universite Paris Sud, Clamart, France
J Cardiovasc Pharmacol 49:1-5. 2007..Selected patients with PAH can be safely transitioned from intravenous epoprostenol to intravenous treprostinil using a rapid switch protocol...
[Treatment of pulmonary arterial hypertension in 2011: what's new since the 2009 ERS/ESC guidelines?]Laurent Savale
Universite Paris Sud, Faculte de Medecine, Le Kremlin Bicetre, France
Presse Med 40:1S54-60. 2011..Finally, clinical trials evaluating combinations of treatments have shown encouraging results...
Pulmonary hypertension: CT of the chest in pulmonary venoocclusive diseaseArnaud Resten
Service de Radiologie, UPRES EA 2705 Maladies vasculaires pulmonaires, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud, 157 rue de la Porte de Trivaux, Clamart 92140, France
AJR Am J Roentgenol 183:65-70. 2004..The aim of our study was to evaluate this disease noninvasively using CT of the chest...
Clinical challenges in pulmonary hypertension: Roger S. Mitchell lectureSteeve Provencher
Centre des Maladies Vasculaires Pulmonaires UP RES EA 2705, Service de Pneumologie et Reanimation Respiratoire, AP HP Université Paris Sud XI, Hopital Antoine Beclere, Clamart, France
Chest 128:622S-628S. 2005..Early detection and adequate clinical classification of the disease, better assessment of patients' prognosis, and improved therapeutic strategies are important challenges for clinicians in coming years...
Assessing effectiveness of pulmonary arterial hypertension therapies in daily practiceOlivier Sitbon
Service de Pneumologie, Hopital Antoine Beclere, Clamart, France
Curr Opin Pulm Med 16:S21-6. 2010..Treatment goals need to be carefully defined in order to correctly measure whether a treatment is successful and indicate when additional treatment is required...
Continuous subcutaneous infusion of treprostinil, a prostacyclin analogue, in patients with pulmonary arterial hypertension: a double-blind, randomized, placebo-controlled trialGerald Simonneau
Division of Pulmonary and Critical Care Medicine, Antoine Beclere Hospital, Clamart, Paris Sud University, Clamart, France
Am J Respir Crit Care Med 165:800-4. 2002..We conclude that chronic subcutaneous infusion of treprostinil is an effective treatment with an acceptable safety profile in patients with pulmonary arterial hypertension...
Clinical classification of pulmonary hypertensionGerald Simonneau
Department of Pulmonary and Critical Medicine, University of Paris Sud, Paris, France
J Am Coll Cardiol 43:5S-12S. 2004....
Pulmonary hypertension in patients with neurofibromatosis type IDavid Montani
Faculte de Medecine, Universite Paris Sud, Kremlin Bicetre, France
Medicine (Baltimore) 90:201-11. 2011..Further studies are needed to better understand the pathophysiology and the role, if any, of neurofibromin in NF1-associated PH...
Endothelin-1/endothelin-3 ratio: a potential prognostic factor of pulmonary arterial hypertensionDavid Montani
Centre des Maladies Vasculaires Pulmonaires, UPRES EA 2705, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Université Paris Sud 157 rue de la Porte de Trivaux, 92140 Clamart, France
Chest 131:101-8. 2007..Endothelin (ET)-1 has been shown to play a significant pathogenic role in PAH. ET-3 has not yet been investigated in PAH...
Fibrous remodeling of the pulmonary venous system in pulmonary arterial hypertension associated with connective tissue diseasesPeter Dorfmuller
Service d Anatomie et de Cytologie Pathologiques, Centre Hospitalier Universitaire Pitie Salpetriere, 47 83, Boulevard de l Hopital, F 75651 Paris Cedex 13, France
Hum Pathol 38:893-902. 2007....
Evaluation of various empirical formulas for estimating mean pulmonary artery pressure by using systolic pulmonary artery pressure in adultsDenis Chemla
Paris Sud University EA4046, Medical Intensive Care Unit, Paris, France
Chest 135:760-8. 2009..Our study evaluated the accuracy and precision of various empirical formulas relating mPAP and sPAP in resting adults...
[Pulmonary arterial hypertension and sickle cell disease]Laurent Savale
Universite Paris Sud, Faculte de Medecine, 94276 Kremlin Bicêtre, France
Presse Med 42:338-46. 2013..5m/s is used. At present, no specific treatments for pulmonary arterial hypertension is currently approved for the treatment of PAH associated with sickle cell disease due to lack of data in this specific population...
Drug Insight: endothelin-receptor antagonists for pulmonary arterial hypertension in systemic rheumatic diseasesMarc Humbert
Center for Pulmonary Vascular Diseases, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud, France
Nat Clin Pract Rheumatol 1:93-101. 2005..This article reviews PAH associated with systemic rheumatic diseases and describes the role of ERAs in this setting...
Diagnostic value of D-dimer in patients with suspected pulmonary embolism: results from a multicentre outcome studyFlorence Parent
Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Clamart, France
Thromb Res 120:195-200. 2007..However, their role as an exclusionary first-line test is still uncertain, mainly because accuracy of the test varies according to the assay and the studied population...
Pulmonary artery pressure-flow relations after prostacyclin in primary pulmonary hypertensionVincent Castelain
Department of Pulmonary Medicine (UPRES 2705, , Clamart, France
Am J Respir Crit Care Med 165:338-40. 2002..1 mm Hg/L/min/m(2) (p < 0.01). These results suggest that the improvement in exercise tolerance seen after 6 wk of prostacyclin therapy may be ascribable to a decrease in incremental pulmonary vascular resistance during exercise...
Severe pulmonary arterial hypertension in type 1 glycogen storage diseaseMarc Humbert
Service de Pneumologie, Centre des Maladies Vasculaires Pulmonaires, Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, 92140 Clamart, France
Eur J Pediatr 161:S93-6. 2002....
CX(3)C chemokine fractalkine in pulmonary arterial hypertensionKarl Balabanian
INSERM U131, UPRES EA2705, Centre des Maladies Vasculaires Pulmonaires, Service de Pneumologie et Reanimation Respiratoire, Institut Paris Sud sur les Cytokines, Hopital Antoine Beclere, Universite Paris Sud, Clamart, France
Am J Respir Crit Care Med 165:1419-25. 2002..Fractalkine mRNA and protein product are expressed in pulmonary artery endothelial cells. We conclude that inflammatory mechanisms involving chemokine fractalkine and its receptor CX(3)CR1 may have a role in the natural history of PAH...
Pulmonary arterial hypertension masquerading as severe refractory asthmaL Achouh
Universite Paris Sud 11, Centre National de Référence de l Hypertension Artérielle Pulmonaire, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Clamart, France
Eur Respir J 32:513-6. 2008..The present observations add dilatation of the central pulmonary arteries with compression of the mainstem bronchi to the list of masqueraders of asthma in patients with pulmonary arterial hypertension...
[Postembolic pulmonary hypertension]X Jais
Centre de Référence de l Hypertension Artérielle Pulmonaire, Unité Propre de Recherche de l Enseignement Supérieur EA2705, Hopital Antoine Beclere, Universite Paris Sud, Assistance Publique Hopitaux de Paris, Clamart, France
Rev Mal Respir 24:497-508. 2007....
Treatment of patients with mildly symptomatic pulmonary arterial hypertension with bosentan (EARLY study): a double-blind, randomised controlled trialN Galie
Institute of Cardiology, University of Bologna, Bologna, Italy
Lancet 371:2093-100. 2008..This study was designed to assess the effect of the dual endothelin receptor antagonist bosentan in patients with WHO FC II pulmonary arterial hypertension...
Changes in exercise haemodynamics during treatment in pulmonary arterial hypertensionS Provencher
Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, 92140 Clamart, France
Eur Respir J 32:393-8. 2008..Improvement in exercise tolerance with chronic therapy is independently related to improvement in pulmonary haemodynamics measured in exercise but not in resting conditions...
Pulmonary artery pulse pressure and wave reflection in chronic pulmonary thromboembolism and primary pulmonary hypertensionV Castelain
Service de Pneumologie, , , Assistance Publique-H pitaux de Paris, Clamart, France
J Am Coll Cardiol 37:1085-92. 2001....
[Pulmonary arterial hypertension]D Montani
Centre des Maladies Vasculaires Pulmonaires, UPRES EA2705, , , , Assistance Publique, , Clamart, France
Rev Mal Respir 22:651-66. 2005..The evolution of therapy from vasodilators to antiproliferative agents reflects the advancement in our understanding of the mechanisms mediating pulmonary arterial hypertension...
[Genetics of pulmonary arterial hypertension: recent data and practical applications]B Sztrymf
UPRES EA 2705, Service de Pneumologie et Reanimation Respiratoire, Centre des Maladies Vasculaires Pulmonaires, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud, France
Rev Mal Respir 22:796-805. 2005..Beside idiopathic PAHT and that associated with other conditions, a familial form has been identified...
Survival in patients with class III idiopathic pulmonary arterial hypertension treated with first line oral bosentan compared with an historical cohort of patients started on intravenous epoprostenolO Sitbon
Centre des Maladies Vasculaires Pulmonaires, Hopital Antoine Beclere, Universite Paris Sud, 157 rue de la Porte de Trivaux, 92141 Clamart, France
Thorax 60:1025-30. 2005....
Survival with first-line bosentan in patients with primary pulmonary hypertensionV V McLaughlin
University of Michigan, 1500 East Medical Center Drive, Women s Hospital, Room L3119, Ann Arbor, MI, USA
Eur Respir J 25:244-9. 2005..First-line bosentan therapy was found to improve survival in patients with advanced primary pulmonary hypertension...
[Treatments for pulmonary arterial hypertension.]D Montani
Centre des Maladies Vasculaires Pulmonaires, UPRES EA2705, , , , , 157, rue de la Porte-de-Trivaux, 92140 Clamart, France
Rev Med Interne 25:720-31. 2004..FUTURE PROSPECTS AND PROJECTS: The evolution of therapy from vasodilators to antiproliferative agents reflects the advancement in our understanding of the mechanisms mediating pulmonary arterial hypertension...
Combination of bosentan with epoprostenol in pulmonary arterial hypertension: BREATHE-2M Humbert
Hopital Antoine Beclere, Assistance Publique, Hopitaux de Paris, Universite Paris Sud, 157 rue de la Porte de Trivaux, 92140, Clamart, France
Eur Respir J 24:353-9. 2004..Several cases of early and late major complications were reported. Additional information is needed to evaluate the risk/benefit ratio of combined bosentan-epoprostenol therapy in pulmonary arterial hypertension...
[Surgical treatment of post-embolism pulmonary hypertension]P Dartevelle
département de chirurgie thoracique vasculaire et transplantation cardio pulmonaire, Hopital Marie Lannelongue, Universite Paris Sud, 133, avenue de la resistance, 92350 Le Plessis Robinson
Rev Pneumol Clin 60:124-34. 2004....
Novel therapeutic perspectives in pulmonary arterial hypertensionM Humbert
Eur Respir J 22:193-4. 2003
[Pulmonary artery hypertension associated with connective tissue diseases]O Sanchez
Centre des Maladies Vasculaires Pulmonaires (UPRES EA 2705, , , 157 rue de la Porte de Trivaux, 92140 Clamart
Presse Med 32:789-99. 2003..IN PRACTICE: PH is a severe complication of connective tissue diseases. Early detection of this complication should allow an earlier and more aggressive therapeutic approach in these patients, before irreversible vascular lesions occur...
[Chronic pulmonary heart disease: therapeutic indications]R Azarian
, , Clamart
Arch Mal Coeur Vaiss 88:1799-805. 1995..Of all the causes of pulmonary hypertension, chronic thromboembolic cor pulmonary should be systematically looked for because curative surgical treatment is possible in some cases...
[Economic assessment of the use of tinzaparin in the treatment of acute pulmonary embolism in France]D Lewis
NERA Londres, 15 Stratford Place, Londres WIN 9AF, Royaume-Uni
Presse Med 30:1539-48. 2001..CONCLUSION: Tinzaparin reduced health care costs for pulmonary embolism due to easier administration, less complex laboratory tests, and personnel time savings. The robustness of the results was confirmed by the sensitivity analysis...
Clinical and molecular genetic features of pulmonary hypertension in patients with hereditary hemorrhagic telangiectasiaR C Trembath
Department of Medicine, University of Leicester, United Kingdom
N Engl J Med 345:325-34. 2001..Because patients with hereditary hemorrhagic telangiectasia may have lung disease that is indistinguishable from primary pulmonary hypertension, we investigated the genetic basis of lung disease in these patients...
[Treatment for pulmonary arterial hypertension under the new French hospital financing system. Recommendations of the Pulmonary Vascular Diseases Working Group of the French Society of Pulmonary Medicine]O Sitbon
Centre de référence national sur l HTAP, Service de Pneumologie et Reanimation, UPRES EA2705, Universite Paris Sud, Hopital Antoine Beclere, AP HP, Clamart
Presse Med 34:1456-64. 2005..The Pulmonary Vascular Diseases working group of the French Society of Pulmonary Medicine has developed guidelines for the best practices in use of these drugs...
The efficacy of bosentan in inoperable chronic thromboembolic pulmonary hypertension: a 1-year follow-up studyR J Hughes
Pulmonary Vascular Diseases Unit, Papworth Hospital, Cambridgeshire, CB3 8RE, UK
Eur Respir J 28:138-43. 2006....
Heart rate responses during the 6-minute walk test in pulmonary arterial hypertensionS Provencher
Centre des Maladies Vasculaires Pulmonaires UPRES EA 2705, Service de Pneumologie et Reanimation Respiratoire, AP HP Université Paris Sud IX, Hopital Antoine Beclere, Clamart, France
Eur Respir J 27:114-20. 2006..The lack of chronotropic response may reflect the loss in normal physiological reserve in more unwell patients...
Long-term outcome in pulmonary arterial hypertension patients treated with subcutaneous treprostinilR J Barst
Columbia University College of Physicians and Surgeons, 3959 Broadway, BHN 2 255, New York, NY 10032, USA
Eur Respir J 28:1195-203. 2006..In contrast, predicted survival was 69-38% over 1-4 yrs. The safety profile for long-term subcutaneous treprostinil was consistent with previous short-term trials with no unexpected adverse events...
Bosentan for the treatment of pulmonary arterial hypertension associated with congenital heart defectsO Sitbon
Hopital Antoine Beclere, Service de Pneumologie, Clamart, France
Eur J Clin Invest 36:25-31. 2006..Pre-clinical data support the rationale for the potential benefit of bosentan in PAH associated with congenital heart disease (CHD)...
[Pulmonary hypertension associated with connective tissue diseases]O Sanchez
, UPRES EA 2705 Maladies vasculaires pulmonaires, , 157, rue de la Porte de Trivaux, 92141 Clamart, France
Rev Med Interne 23:41-54. 2002..The role of immunosuppressive therapy has to be defined...
[Pulmonary hypertension complicating systemic diseases other than connective tissue diseases]O Sanchez
Centre des Maladies Vasculaires Pulmonaires (UPRES EA 2705, , , 157 rue de la Porte de Trivaux, 92140 Clamart
Presse Med 32:800-3. 2003..The physiopathological mechanisms responsible are unclear (specific parenchymal fibrosis, isolated vascular involvement...). Globally, available treatments are disappointing...
[Pulmonary arterial hypertension of chronic thromboembolic origin; therapeutic indications]R Azarian
Service de Pneumologie, , Clamart
Arch Mal Coeur Vaiss 87:1709-13. 1994..Chronic thromboembolism should be systematically investigated as the cause of pulmonary hypertension considering that in selected cases, curative surgery is possible...
Dendritic cell recruitment in lesions of human and experimental pulmonary hypertensionF Perros
UPRES EA2705, Service de Pneumologie, Centre National de Référence de l Hypertension Artérielle Pulmonaire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud, France
Eur Respir J 29:462-8. 2007..The results support the concept that immature dendritic cells accumulate in remodelled pulmonary vessels and hence could be involved in the immunopathology of pulmonary hypertension...
BMPR2 germline mutations in pulmonary hypertension associated with fenfluramine derivativesM Humbert
Service de Pneumologie, Hĵpital Antoine Béclère, Clamart, France
Eur Respir J 20:518-23. 2002....
Function of the serotonin 5-hydroxytryptamine 2B receptor in pulmonary hypertensionJ M Launay
CR C Bernard Pathologie expérimentale et communications cellulaires, IFR6, Services de Biochimie et d Angio Hématologie, Hôpital Lariboisière AP HP, Paris, France
Nat Med 8:1129-35. 2002..These data show that activation of 5-HT(2B) receptors is a limiting step in the development of pulmonary hypertension...
[Investigation of pulmonary hypertension]D Natali
Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud 11, 92141 Clamart Cedex, France
Rev Pneumol Clin 64:151-61. 2008..Characterization of PH is essential in the management of PH because it determines the appropriate treatment: an etiological treatment in passive, obstructive or hypoxemic PH, or vasodilatator and antiproliferative therapies in PAH...
Pulmonary arterial hypertension and type-I glycogen-storage disease: the serotonin hypothesisM Humbert
Unité Propre de Recherche de l Enseignement Supérieur 2705, Centre des Maladies Vasculaires Pulmonaires, Hĵpital Antoine Béclère, Universite Paris Sud, Clamart, France
Eur Respir J 20:59-65. 2002..4 nmol x L(-1)). It is concluded that type-Ia glycogen-storage disease may be another condition in which abnormal handling of serotonin is one event in a multistep process leading to severe pulmonary arterial hypertension...
[Pulmonary arterial hypertension due to tumor emboli]J M Dot
Centre national de référence de l hypertension pulmonaire, UPRES EA 2705, Service de Pneumologie et Reanimation Respiratoire, Hopital Antoine Beclere, Assistance Publique Hopitaux de Paris, Universite Paris Sud, Clamart, France
Rev Mal Respir 24:359-66. 2007..Pulmonary arterial hypertension (PAH) is rare in the presence of malignancy and tumour embolisation is one of several possible pathological mechanisms...
[What is your diagnosis?]S Espinoza
Service de Radiologie, Hopital Antoine Beclere, 157 rue de la Porte de Trivaux, Clamart
J Radiol 88:409. 2007
Role of nitric oxide in hepatopulmonary syndrome in cirrhotic ratsH Nunes
Surgical Research Laboratory-UPRES (EA-2705, Marie Lannelongue Surgical Center, Paris South University, Paris, France
Am J Respir Crit Care Med 164:879-85. 2001....
Serotonin transporter overexpression is responsible for pulmonary artery smooth muscle hyperplasia in primary pulmonary hypertensionS Eddahibi
, , AP-HP, , France
J Clin Invest 108:1141-50. 2001..We conclude that 5-HTT activity plays a key role in the pathogenesis of PA-SMC proliferation in PPH and that a 5HTT polymorphism confers susceptibility to PPH...
