Jérôme Harambat

Summary

Affiliation: CHU de Bordeaux
Country: France

Publications

  1. pmc Primary hyperoxaluria
    Jérôme Harambat
    Service de Pediatrie, Centre de référence Maladies Rénales Rares du Sud Ouest, Centre Hospitalier Universitaire de Bordeaux, 33076 Bordeaux, France
    Int J Nephrol 2011:864580. 2011
  2. doi Disparities in policies, practices and rates of pediatric kidney transplantation in Europe
    J Harambat
    ESPN ERA EDTA Registry, Department of Medical Informatics, Academic Medical Center, Amsterdam, The Netherlands
    Am J Transplant 13:2066-74. 2013
  3. doi Prediction of steroid-sparing agent use in childhood idiopathic nephrotic syndrome
    Jérôme Harambat
    Service de Pediatrie, Centre de référence Maladies Rénales Rares du Sud Ouest, Centre Hospitalier Universitaire de Bordeaux, Place Amelie Raba Leon, 33076, Bordeaux, France
    Pediatr Nephrol 28:631-8. 2013
  4. doi Adenine phosphoribosyltransferase deficiency in children
    Jérôme Harambat
    Service de Pediatrie, Centre Hospitalier Universitaire de Bordeaux, Centre de référence Maladies Rénales Rares du Sud Ouest, Bordeaux, France
    Pediatr Nephrol 27:571-9. 2012
  5. doi Successful treatment with rituximab for acute refractory thrombotic thrombocytopenic purpura related to acquired ADAMTS13 deficiency: a pediatric report and literature review
    Jérôme Harambat
    Service de Pédiatrie Hôpital Pellegrin Enfants, CHU de Bordeaux and Université de Bordeaux, Bordeaux, France
    Pediatr Crit Care Med 12:e90-3. 2011
  6. pmc Characteristics and outcomes of children with primary oxalosis requiring renal replacement therapy
    Jérôme Harambat
    ESPN ERA EDTA Registry, Department of Medical Informatics, Academic Medical Center, Amsterdam, The Netherlands
    Clin J Am Soc Nephrol 7:458-65. 2012
  7. doi Long-term effects of cyclophosphamide therapy in steroid-dependent or frequently relapsing idiopathic nephrotic syndrome
    Benoit Cammas
    Centre Hospitalier Universitaire de Bordeaux, Service de Pediatrie, Centre de référence Maladies Rénales Rares du Sud Ouest, Bordeaux, France
    Nephrol Dial Transplant 26:178-84. 2011
  8. doi Severe transient ADAMTS13 deficiency in pneumococcal-associated hemolytic uremic syndrome
    Sybille Pelras
    Service de Pediatrie, Hôpital Pellegrin Enfants, Centre Hospitalier Universitaire, Bordeaux, France
    Pediatr Nephrol 26:631-5. 2011
  9. doi Effect of conservative treatment on the renal outcome of children with primary hyperoxaluria type 1
    Sonia Fargue
    Service de Pediatrie, Centre de Référence des Maladies Rénales Rares, Hospices Civils de Lyon and Université Lyon 1, Lyon, France
    Kidney Int 76:767-73. 2009
  10. doi Maximizing growth in children after renal transplantation
    Pierre Cochat
    Service de Pediatrie, Centre de Référence des Maladies Rénales Rares and Inserm U820, Hospices Civils de Lyon and Université de Lyon, Lyon, France
    Transplantation 88:1321-2. 2009

Collaborators

Detail Information

Publications17

  1. pmc Primary hyperoxaluria
    Jérôme Harambat
    Service de Pediatrie, Centre de référence Maladies Rénales Rares du Sud Ouest, Centre Hospitalier Universitaire de Bordeaux, 33076 Bordeaux, France
    Int J Nephrol 2011:864580. 2011
    ..In end-stage renal disease patients, the best outcomes have been achieved with combined liver-kidney transplantation which corrects the enzyme defect...
  2. doi Disparities in policies, practices and rates of pediatric kidney transplantation in Europe
    J Harambat
    ESPN ERA EDTA Registry, Department of Medical Informatics, Academic Medical Center, Amsterdam, The Netherlands
    Am J Transplant 13:2066-74. 2013
    ..The lack of harmonization in kidney allocation to children raises medical and ethical issues. Harmonization of pediatric allocation policies should be prioritized. ..
  3. doi Prediction of steroid-sparing agent use in childhood idiopathic nephrotic syndrome
    Jérôme Harambat
    Service de Pediatrie, Centre de référence Maladies Rénales Rares du Sud Ouest, Centre Hospitalier Universitaire de Bordeaux, Place Amelie Raba Leon, 33076, Bordeaux, France
    Pediatr Nephrol 28:631-8. 2013
    ..The aim of this study was to identify predictors of the need for SSA and derive a predictive model...
  4. doi Adenine phosphoribosyltransferase deficiency in children
    Jérôme Harambat
    Service de Pediatrie, Centre Hospitalier Universitaire de Bordeaux, Centre de référence Maladies Rénales Rares du Sud Ouest, Bordeaux, France
    Pediatr Nephrol 27:571-9. 2012
    ..Based on these results, we conclude that an excellent outcome can be achieved in children with APRT deficiency who receive the proper treatment...
  5. doi Successful treatment with rituximab for acute refractory thrombotic thrombocytopenic purpura related to acquired ADAMTS13 deficiency: a pediatric report and literature review
    Jérôme Harambat
    Service de Pédiatrie Hôpital Pellegrin Enfants, CHU de Bordeaux and Université de Bordeaux, Bordeaux, France
    Pediatr Crit Care Med 12:e90-3. 2011
    ..To report the case of a child with severe autoimmune thrombotic thrombocytopenic purpura (TTP) resistant to plasma exchange and steroids who was successfully treated with rituximab...
  6. pmc Characteristics and outcomes of children with primary oxalosis requiring renal replacement therapy
    Jérôme Harambat
    ESPN ERA EDTA Registry, Department of Medical Informatics, Academic Medical Center, Amsterdam, The Netherlands
    Clin J Am Soc Nephrol 7:458-65. 2012
    ..Primary hyperoxaluria (PH) as a cause of ESRD in children is believed to have poor outcomes. Data on management and outcomes of these children remain scarce...
  7. doi Long-term effects of cyclophosphamide therapy in steroid-dependent or frequently relapsing idiopathic nephrotic syndrome
    Benoit Cammas
    Centre Hospitalier Universitaire de Bordeaux, Service de Pediatrie, Centre de référence Maladies Rénales Rares du Sud Ouest, Bordeaux, France
    Nephrol Dial Transplant 26:178-84. 2011
    ..Little is known about prognostic factors in SDNS and FRNS treated by CYP. The objectives of this study are to determine long-term outcomes and factors associated with sustained remission in these patients...
  8. doi Severe transient ADAMTS13 deficiency in pneumococcal-associated hemolytic uremic syndrome
    Sybille Pelras
    Service de Pediatrie, Hôpital Pellegrin Enfants, Centre Hospitalier Universitaire, Bordeaux, France
    Pediatr Nephrol 26:631-5. 2011
    ..Severe ADAMTS13 deficiency appears to be a manifestation of transient endothelial cell injury in the context of severe sepsis, including invasive p-HUS. The choice of appropriate therapy should not be based on this finding...
  9. doi Effect of conservative treatment on the renal outcome of children with primary hyperoxaluria type 1
    Sonia Fargue
    Service de Pediatrie, Centre de Référence des Maladies Rénales Rares, Hospices Civils de Lyon and Université Lyon 1, Lyon, France
    Kidney Int 76:767-73. 2009
    ..7 per year. Our study strongly suggests that early and aggressive conservative management may preserve renal function of compliant children with this disorder, thereby avoiding dialysis and postponing transplantation...
  10. doi Maximizing growth in children after renal transplantation
    Pierre Cochat
    Service de Pediatrie, Centre de Référence des Maladies Rénales Rares and Inserm U820, Hospices Civils de Lyon and Université de Lyon, Lyon, France
    Transplantation 88:1321-2. 2009
    ....
  11. doi Genotype-phenotype correlation in primary hyperoxaluria type 1: the p.Gly170Arg AGXT mutation is associated with a better outcome
    Jérôme Harambat
    Service de Pediatrie, Centre de Référence des Maladies Rénales Rares du Sud Ouest, Centre Hospitalier Universitaire, Bordeaux, France
    Kidney Int 77:443-9. 2010
    ..Our results underscore the severe prognosis of primary hyperoxaluria type 1 and the necessity for early diagnosis and treatment, as well as confirm a better prognosis of the p.Gly170Arg mutation...
  12. pmc Epidemiology of chronic kidney disease in children
    Jérôme Harambat
    ESPN ERA EDTA Registry, Department of Medical Informatics, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands
    Pediatr Nephrol 27:363-73. 2012
    ..While the survival rate of children with ERSD has improved, it remains about 30 times lower than that of healthy peers. Children now mainly die of cardiovascular causes and infection rather than from renal failure...
  13. doi Hemolytic uremic syndrome complicating Mycoplasma pneumoniae infection
    Astrid Godron
    Service de Pediatrie, Centre de référence Maladies Rénales Rares du Sud Ouest, Hôpital Pellegrin Enfants, CHU de Bordeaux, France
    Pediatr Nephrol 28:2057-60. 2013
    ..Mycoplasma pneumoniae can cause various extrapulmonary manifestations but, to our knowledge, no case of Mycoplasma pneumoniae associated with hemolytic uremic syndrome (HUS) has been reported...
  14. doi Long-term critical issues in pediatric renal transplant recipients: a single-center experience
    Jérôme Harambat
    Service de néphrologie et rhumatologie pédiatrique, Centre de Référence des Maladies Rénales Rares, Hopital Femme Mere Enfant, Hospices Civils de Lyon, Bron, France
    Transpl Int 26:154-61. 2013
    ..Excellent long-term outcomes can be achieved in pediatric renal Tx, but specific problems such as malignancies, growth, and social outcome remain challenging...
  15. doi Renal impairment in children with cystic fibrosis
    Annick Andrieux
    CHU de Bordeaux, Centre de Ressources et de Compétences de la Mucoviscidose pédiatrique, Hôpital Pellegrin Enfants, Bordeaux, France
    J Cyst Fibros 9:263-8. 2010
    ..Due to the improvement in life expectancy in cystic fibrosis (CF), co-morbidities such as renal function impairment may be more frequent...
  16. pmc Invasive fungal disease in PICU: epidemiology and risk factors
    Olivier Brissaud
    Pediatric and Neonatal Intensive Care Unit, The Children s Hospital of Bordeaux, Place Amelie Raba Leon, 33076 Bordeaux Cedex, France
    Ann Intensive Care 2:6. 2012
    ..In children, the mortality rate for invasive aspergillosis is 2.5 to 3.5 higher than for invasive candidiasis (respectively 70% vs. 20% and 30%)...
  17. doi [Phenotypic heterogeneity of TCF2's gene mutation coding for HNF-1 beta in a single family]
    Claire Rigothier
    Services de néphrologie et de pédiatrie, Centre de Référence des Maladies Rénales Rares du Sud Ouest, Universite de Bordeaux, CHU de Bordeaux, Bordeaux, France
    Nephrol Ther 5:287-91. 2009
    ....