Research Topics
Species | Grace YoonSummaryAffiliation: University of Toronto Country: Canada Publications
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Detail Information
Publications
Cardiac transplantation in Friedreich ataxiaGrace Yoon
Division of Clinical and Metabolic Genetics, Department of Pediatrics, The Hospital for Sick Children, University of Toronto, Toronto, ON, Canada
J Child Neurol 27:1193-6. 2012..We review the ethical issues considered during the process leading to the decision to offer cardiac transplantation...
Neurological complications of cardio-facio-cutaneous syndromeGrace Yoon
Department of Pediatrics, Division of Medical Genetics, The Hospital for Sick Children, University of Toronto, Canada
Dev Med Child Neurol 49:894-9. 2007..Seizures were present in 15 participants. No specific genotype-phenotype correlation was observed...
Novel mutation in ARX associated with early hand preference and a mild phenotypeGhassan Abu Kuwaik
Division of Neurology, Department of Pediatrics, The Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada
J Dev Behav Pediatr 33:586-8. 2012....
Definition of a critical genetic interval related to kidney abnormalities in the Potocki-Lupski syndromeElaine Suk Ying Goh
Division of Clinical and Metabolic Genetics, The Hospital for Sick Children and University of Toronto, Toronto, Ontario, Canada
Am J Med Genet A 158:1579-88. 2012..285 Mb critical region, including the FLCN gene that may be important for development of renal abnormalities in patients with this duplication...
Diagnostic approach to childhood-onset cerebellar atrophy: a 10-year retrospective study of 300 patientsAlmundher Al-Maawali
Division of Clinical and Metabolic Genetics, The Hospital for Sick Children, University of Toronto, Toronto, ON, Canada
J Child Neurol 27:1121-32. 2012..We review the common causes of cerebellar atrophy in childhood and propose a diagnostic approach based on correlating specific neuroimaging patterns with clinical and genetic diagnoses...
Friedreich ataxia presenting as sudden cardiac death in childhood: clinical, genetic and pathological correlation, with implications for genetic testing and counsellingNada Quercia
Division of Clinical and Metabolic Genetics, Hospital for Sick Children, University of Toronto, Toronto, Canada
Neuromuscul Disord 20:340-2. 2010..Molecular genetic testing subsequently confirmed the diagnosis of Friedreich ataxia. To our knowledge, this is the first report of Friedreich ataxia presenting as sudden cardiac death in early childhood...
2q23 de novo microdeletion involving the MBD5 gene in a patient with developmental delay, postnatal microcephaly and distinct facial featuresBrian H Y Chung
Division of Clinical and Metabolic Genetics, Department of Pediatrics, Hospital for Sick Children, Toronto, Ontario, Canada
Am J Med Genet A 155:424-9. 2011..Her speech was dysarthric, and she demonstrated repetitive hand movements. In this article, we compare the clinical features of our patient with previously reported cases with a 2q23.1 deletion...
Mosaic microdeletion 18q21 as a cause of mental retardationDimitri J Stavropoulos
Department of Pediatric Laboratory Medicine, Hospital for Sick Children, Toronto, Ontario, Canada
Eur J Med Genet 53:396-9. 2010....
Cockayne syndrome caused by paternally inherited 5 Mb deletion of 10q11.2 and a frameshift mutation of ERCC6Shailly Jain Ghai
Division of Clinical and Metabolic Genetics, The Hospital for Sick Children, University of Toronto, 555 University Avenue, Toronto, ON M5G 1X8, Canada
Eur J Med Genet 54:272-6. 2011..We report a patient with a clinical phenotype of severe infantile CS who has a paternally inherited 5 Mb deletion of 10q11.2 resulting in loss of one allele and a previously unreported frameshift mutation of ERCC6 on the maternal allele...
Mitochondrial mimicry of multiple system atrophy of the cerebellar subtypeArpan R Mehta
Movement Disorder Clinic, Toronto Western Hospital, University of Toronto, Toronto, Canada
Mov Disord 26:753-5. 2011..We describe a patient with clinical and radiological findings suggestive of multiple system atrophy of the cerebellar subtype (MSA-C)...
Intermediate-dose idebenone and quality of life in Friedreich ataxiaJohn F Brandsema
Division of Neurology, The Hospital for Sick Children, University of Toronto, Toronto, Canada
Pediatr Neurol 42:338-42. 2010..Functional ability, as measured by activities of daily living scores, appeared to have the most influence on the perception of physical quality of life, which may be important in planning future therapeutic trials...
Magnetic resonance imaging of a unique mutation in a family with Pelizaeus-Merzbacher diseaseElka Miller
Division of Neuroradiology, Department of Diagnostic Imaging, The Hospital for Sick Children, Ontario, Canada
Am J Med Genet A 152:748-52. 2010..The brain MRI appearances in this unique deletion, using newer MR imaging, are described...
Ataxia and pancytopenia caused by a mutation in TINF2Elena Tsangaris
Cell Biology Program, Research Institute, University of Toronto, Toronto, ON, Canada
Hum Genet 124:507-13. 2008..845G>A (Arg282His) in TINF2, a gene recently reported to be mutated in a subset of patients with autosomal dominant dyskeratosis congenita. We propose that some cases of ataxia-pancytopenia may be affected by DC...
Andersen-Tawil syndrome: a model of clinical variability, pleiotropy, and genetic heterogeneityMatthew R Donaldson
Department of Human Molecular Biology and Genetics, University of Utah, Salt Lake City, USA
Ann Med 36:92-7. 2004..Other ATS genes likely share a common pathway or function with Kir2.1 or facilitate the activity of this ion channel. In this review, we explore hypotheses explaining the pathogenesis, expression, and variability of ATS...
