Research Topics
| Sung Yun PaiSummaryAffiliation: Harvard University Country: USA Publications
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Detail Information
Publications
Allogeneic transplantation successfully corrects immune defects, but not susceptibility to colitis, in a patient with nuclear factor-kappaB essential modulator deficiencySung Yun Pai
Division of Hematology Oncology, Children s Hospital Boston, Boston, MA 02115, USA
J Allergy Clin Immunol 122:1113-1118.e1. 2008..Boys with X-linked ectodermal dysplasia and immunodeficiency caused by mutations of nuclear factor-kappaB essential modulator have defects in innate and adaptive immunity, and some have colitis...
Allogeneic hematopoietic stem cell transplantation for X-linked ectodermal dysplasia and immunodeficiency: case report and review of outcomesPerdita Permaul
Division of Immunology, Children s Hospital Boston, Boston, MA, USA
Immunol Res 44:89-98. 2009..We describe his treatment course as well as reconstitution of immune function and correction of osteopetrosis post-HSCT, and review the cases of allogeneic HSCT reported to date in the literature...
IL-21 is the primary common ? chain-binding cytokine required for human B-cell differentiation in vivoMike Recher
Division of Immunology, Children s Hospital, Harvard Medical School, Boston, MA, USA
Blood 118:6824-35. 2011..Furthermore, in vitro stimulation with CD40L/IL-21 can predict in vivo B-cell immunity in IL2RG/JAK3 SCID after transplantation...
p53+/mdm2- atypical lipomatous tumor/well-differentiated liposarcoma in young children: an early expression of Li-Fraumeni syndromeLarisa V Debelenko
Department of Pathology, Children s Hospital Boston, 300 Longwood Avenue, Boston, MA 02115, USA
Pediatr Dev Pathol 13:218-24. 2010..Recognition of this lesion and its association is important for early diagnosis and subsequent tumor surveillance in the proband and affected family members...
Hematopoietic cell transplantation for Wiskott-Aldrich syndrome: advances in biology and future directions for treatmentSung Yun Pai
Division of Hematology Oncology, Children s Hospital Boston, Karp Family Research Laboratories, 8th Floor, Room 8214, 1 Blackfan Circle, Boston, MA 02115, USA
Immunol Allergy Clin North Am 30:179-94. 2010..The current short- and long-term toxicities of HCT are the main stumbling block for the ability to cure every patient with WAS and X-linked thrombocytopenia, and much remains to be done...
