Research Topics
Species | Veronika VaclavikSummaryCountry: UK Publications
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Publications
Autofluorescence imaging in age-related macular degeneration complicated by choroidal neovascularization: a prospective studyVeronika Vaclavik
Moorfields Eye Hospital, London, United Kingdom
Ophthalmology 115:342-6. 2008....
Autofluorescence findings in acute exudative polymorphous vitelliform maculopathyVeronika Vaclavik
Division of Molecular Genetics, Institute of Ophthalmology, University College London, 11-43 Bath Street, London, England
Arch Ophthalmol 125:274-7. 2007
Retinal dystrophy in the oculo-auricular syndrome due to HMX1 mutationV Vaclavik
Jules Gonin Eye Hospital, Lausanne, Switzerland
Ophthalmic Genet 32:114-7. 2011..To report on the clinical and electrophysiological findings in a patient with oculo-auricular syndrome due to HMX1 mutation, with a follow-up of 12 years...
Variable phenotypic expressivity in a Swiss family with autosomal dominant retinitis pigmentosa due to a T494M mutation in the PRPF3 geneVeronika Vaclavik
Hopital Ophtalmique Jules Gonin, Oculogenetic unit 15, Lausanne, Switzerland
Mol Vis 16:467-75. 2010....
Autosomal Dominant Retinitis Pigmentosa with Intrafamilial Variability and Incomplete Penetrance in Two Families Carrying Mutations in PRPF8Cecilia G Maubaret
Institute of Ophthalmology, University College London, London, United Kingdom
Invest Ophthalmol Vis Sci 52:9304-9. 2011..Conclusions. This is the first report of marked intrafamilial variability associated with mutations in the PRPF8 gene, including incomplete penetrance. PRPF8 mutations should be suspected in patients with adRP and variable expressivity...
Phenotypic variation in enhanced S-cone syndromeIsabelle Audo
Department of Electrophysiology, Moorfields Eye Hospital, 162 City Road, London, United Kingdom
Invest Ophthalmol Vis Sci 49:2082-93. 2008..To characterize the clinical, psychophysical, and electrophysiological phenotype of 19 patients with enhanced S-cone syndrome (ESCS) and relate the phenotype to the underlying genetic mutation...
Novel phenotypic and genotypic findings in X-linked retinoschisisStephen H Tsang
Departments of Clinical Ophthalmology and Electrophysiology, Moorfields Eye Hospital, 162 City Road, London, England
Arch Ophthalmol 125:259-67. 2007..To describe atypical phenotypes associated with the retinoschisis (X-linked, juvenile) 1 mutation (RS1)...
Mutations in the gene coding for the pre-mRNA splicing factor, PRPF31, in patients with autosomal dominant retinitis pigmentosaNaushin H Waseem
Department of Molecular Genetics, Institute of Ophthalmology, University College London, London, United Kingdom
Invest Ophthalmol Vis Sci 48:1330-4. 2007..The purpose of this study was to identify PRPF31 mutations in a cohort of 118 cases of autosomal dominant retinitis pigmentosa and determine the genotype-phenotype correlation emerging from the spectrum of mutations in this gene...
Disease mechanism for retinitis pigmentosa (RP11) caused by missense mutations in the splicing factor gene PRPF31Susan E Wilkie
University College London Institute of Ophthalmology, London, United Kingdom
Mol Vis 14:683-90. 2008..Here we examine in further detail the effect of the A216P mutation on splicing function...
Combined grading for choroidal neovascularisation: colour, fluorescein angiography and autofluorescence imagesStela Vujosevic
Fondazione G B Bietti per l Oftalmologia, IRCCS, Via Livenza 3, 00198 Roma, Italy
Graefes Arch Clin Exp Ophthalmol 245:1453-60. 2007..In this study we introduce a new grading model of autofluorescence images (AF), compare it with fluorescein angiography (FFA) and digital colour fundus photos (COL) and test for inter- and intraobserver reliability...
