Research Topics
| Simon JohnsonSummaryAffiliation: University of Nottingham Country: UK Publications
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Detail Information
Publications
Association of MMP-2 polymorphisms with severe and very severe COPD: a case control study of MMPs-1, 9 and 12 in a European populationImran Haq
School of Molecular Medical Sciences, Institute of Genetics, Queen s Medical Centre, University of Nottingham, UK
BMC Med Genet 11:7. 2010..Previous genetic studies of MMPs in COPD have had inadequate coverage of the genes, and have reported conflicting associations of both single nucleotide polymorphisms (SNPs) and SNP haplotypes, plausibly due to under-powered studies...
Clinical experience of lymphangioleiomyomatosis in the UKS R Johnson
Division of Respiratory Medicine, University of Nottingham, City Hospital, Nottingham NG5 1PB, UK
Thorax 55:1052-7. 2000..This study provides data on the natural history of lymphangioleiomyomatosis in the UK and compares this with experience from other centres...
The ERS guidelines for LAM: trying a rationale approach to a rare diseaseSimon R Johnson
Division of Therapeutics and Molecular Medicine and Nottingham NIHR Respiratory Biomedical Research Unit, Nottingham University Hospital NHS Trust, Queens Medical Centre, Nottingham NG7 2UH, United Kingdom
Respir Med 104:S33-41. 2010..It is hoped that these guidelines will result in standardisation of diagnostic criteria and patient management which will further improve clinical care and facilitate research and clinical trials...
Management of rare diseases in respiratory medicineSimon R Johnson
University Hospital, Queens Medical Centre, Nottingham
Clin Med 7:447-8. 2007
LymphangioleiomyomatosisS R Johnson
Division of Therapeutics and Molecular Medicine, University Hospital, Queens Medical Centre, Nottingham NG7 2UH, UK
Eur Respir J 27:1056-65. 2006..Trials of rapamycin in lymphangioleiomyomatosis are currently underway and offer hope of evidence-based treatment for the disease...
Chronic Respiratory Diseases. Rare lung diseases. IntroductionSimon Johnson
Division of Therapeutics and Molecular Medicine, D Floor, South Block, University Hospital, Queens Medical Centre, Nottingham NG7 2UH, UK
Chron Respir Dis 2:73. 2005
Survival and disease progression in UK patients with lymphangioleiomyomatosisS R Johnson
Division of Therapeutics and Molecular Medicine, Queens Medical Centre, University of Nottingham, Nottingham, UK
Thorax 59:800-3. 2004..In order to provide data for patients and for planning intervention studies, we have looked at the time course of LAM using a national cohort...
An assay to evaluate the long term effects of inflammatory mediators on airway smooth muscle: evidence that TNF(alpha)up-regulates 5-HT(2A) mediated contractionSimon R Johnson
Division of Therapeutics, University Hospital, Nottingham NG7 2UH, UK
Br J Pharmacol 137:943-4. 2002
The TSC-2 product tuberin is expressed in lymphangioleiomyomatosis and angiomyolipomaS R Johnson
Division of Therapeutics, University of Nottingham, UK
Histopathology 40:458-63. 2002..We used immunohistochemistry to test the hypothesis that uncontrolled cellular proliferation in lymphangioleiomyomatosis is the result of reduced tuberin protein expression...
Effects of growth factors and extracellular matrix on survival of human airway smooth muscle cellsA M Freyer
Division of Therapeutics and Institute of Cell Signalling, University Hospital, Nottingham, United Kingdom
Am J Respir Cell Mol Biol 25:569-76. 2001....
Lymphangioleiomyomatosis: a case-control study of perinatal and early life eventsC I Whale
Division of Respiratory Medicine, City Hospital, Nottingham, UK
Thorax 58:979-82. 2003..Being more likely to be an only child and having an increased family history of uterine fibroids may, if confirmed, indicate some differences in reproductive function within the families of affected individuals...
Use of variability in national and regional data to estimate the prevalence of lymphangioleiomyomatosisE C Harknett
Division of Therapeutics and Molecular Medicine and Respiratory Biomedical Research Unit, University of Nottingham, Nottingham, UK
QJM 104:971-9. 2011..As with all rare diseases, obtaining reliable epidemiological data is difficult and requires innovative approaches...
Matrix metalloproteinase-12 (MMP-12) SNP affects MMP activity, lung macrophage infiltration and protects against emphysema in COPDImran Haq
Division of Therapeutics and Molecular Medicine and NIHR Respiratory Biomedical Research Unit, Queens Medical Centre, University of Nottingham, D Floor, South Block, Queen s Medical Centre, Nottingham NG7 2UH, UK
Thorax 66:970-6. 2011..It has previously been shown that individuals homozygous for the A/A allele of rs652438 in MMP-12 are over-represented among patients with severe COPD (n=1517). A study was undertaken to examine the functional basis of these findings...
Discoidin domain receptor 1 regulates bronchial epithelial repair and matrix metalloproteinase productionM E Roberts
Division of Therapeutics and Molecular Medicine, Respiratory Biomedical Research Unit, University of Nottingham, D Floor South Block, Queen s Medical Centre, Nottingham, NG7 2UH, UK
Eur Respir J 37:1482-93. 2011..These data suggest that ECM signalling via DDR1 regulates aspects of bronchial epithelial repair, integrity and MMP expression in the airways...
Pulmonary artery aneurysm and tuberous sclerosisN J Burrows
Queens Medical Centre, University Hospital, Nottingham, UK
Thorax 59:86. 2004
Subcellular distribution of the TSC2 gene product tuberin in human airway smooth muscle cells is driven by multiple localization sequences and is cell-cycle dependentDebbie Clements
Division of Therapeutics and Molecular Medicine, University of Nottingham, Queens Medical Centre, University Hospital, Nottingham NG7 2UH, UK
Am J Physiol Lung Cell Mol Physiol 292:L258-66. 2007..As tuberin has potential roles in proliferation, migration, and cell phenotype, it therefore warrants further investigation in diseases categorized by abnormalities in airway smooth muscle...
Sirolimus therapy in tuberous sclerosis or sporadic lymphangioleiomyomatosisD Mark Davies
N Engl J Med 358:200-3. 2008
Air travel in women with lymphangioleiomyomatosisStacey Pollock-Barziv
Women s College Research Institute, Women s College Hospital, Toronto, Ontario, Canada
Thorax 62:176-80. 2007..A questionnaire-based evaluation of air travel in patients with LAM was conducted to determine experiences aboard commercial aircraft...
Matrix metalloproteinase expression and activity in human airway smooth muscle cellsShona R Elshaw
Division of Therapeutics and Molecular Medicine, University of Nottingham, University Hospital, Queens Medical Centre, Nottingham NG7 2UH
Br J Pharmacol 142:1318-24. 2004..Unstimulated cells secrete excess TIMP 1 and 2, preventing proteolytic activity. MMP-2 can be activated by thrombin which may contribute to airway remodelling...
