Research Topics
Species | F BourdeautSummaryAffiliation: Institut Curie Country: France Publications
| Collaborators
|
Detail Information
Publications
Germline mutations of the paired-like homeobox 2B (PHOX2B) gene in neuroblastomaFranck Bourdeaut
Laboratoire de Pathologie Moléculaire des Cancers, INSERM U 509, Institut Curie, 26 Rue d Ulm, 75248 Paris Cedex 05, France
Cancer Lett 228:51-8. 2005..These observations identify PHOX2B as the first predisposing gene to hereditary neuroblastic tumours...
Alagille syndrome and nephroblastoma: Unusual coincidence of two rare disordersFranck Bourdeaut
Institut Curie, Departement de Pediatrie, Paris F 75246, France
Pediatr Blood Cancer 50:908-11. 2008..In one nephroblastoma an additional somatic 1p36 deletion was present. The link between Alagille syndrome, JAG1 alterations and nephroblastoma is discussed...
VIP hypersecretion as primary or secondary syndrome in neuroblastoma: A retrospective study by the Société Française des Cancers de l'Enfant (SFCE)Franck Bourdeaut
Institut Curie, Departement de Pediatrie, Paris, France
Pediatr Blood Cancer 52:585-90. 2009..Neuroblastic tumors (NTs) are occasionally associated with watery diarrhea, due to Vasoactive Intestinal Peptide (VIP) secretion. Most reports are single cases and suggest a great homogeny within this sub-group of NTs...
[Rhadboid tumours: hSNF/INI1 deficient cancers of early childhood with aggressive behaviour]F Bourdeaut
CHU de Nantes, Service d oncohématologie, 4 Quai Moncousu, 44000 Nantes Cedex, France
Bull Cancer 97:37-45. 2010..Understanding the role of hSNF5/INI1 within the SWI-SNF complex for the epigenetic regulation of transcription might drive the future targeted therapies...
hSNF5/INI1-deficient tumours and rhabdoid tumours are convergent but not fully overlapping entitiesF Bourdeaut
INSERM U509, Laboratoire de Pathologie Moléculaire des Cancers, 26 Rue d Ulm, 75248 Paris Cedex 05, France
J Pathol 211:323-30. 2007..The molecular investigation should be performed in infants when a rhabdoid predisposition syndrome is suspected...
In neuroblastic tumours, Schwann cells do not harbour the genetic alterations of neuroblasts but may nevertheless share the same clonal originF Bourdeaut
INSERM, U830, Section de Recherche, Unité de Génétique et Biologie des Cancers, Institut Curie, Paris, France
Oncogene 27:3066-71. 2008..However, in tumours with both stroma-rich and -poor components, our results suggest that cells from both areas share a common progenitor...
Germline mutations of the paired-like homeobox 2B (PHOX2B) gene in neuroblastomaDelphine Trochet
Unite de Recherches sur les Handicaps Genetiques de l Enfant, INSERM U 393, and Département de Génétique, Hopital Necker Enfants Malades, Paris, France
Am J Hum Genet 74:761-4. 2004..Here, we report on germline mutations of PHOX2B in both a familial case of NB and a patient with the HSCR-NB association. PHOX2B, therefore, stands as the first gene for which germline mutations predispose to NB...
Methylation-associated PHOX2B gene silencing is a rare event in human neuroblastomaLoic de Pontual
Unité de Recherches sur les Handicaps Génétiques de l Enfant INSERM U 781, et Département de Génétique, Universite Rene Descartes, Faculte de Medecine, Hopitaux de Paris, Hopital Necker Enfants Malades, 149, rue de Sevres, 75743 Paris Cedex 15, France
Eur J Cancer 43:2366-72. 2007..9%). Altogether, both germinal and somatic anomalies at the PHOX2B locus are found in NB...
Stepwise occurrence of a complex unbalanced translocation in neuroblastoma leading to insertion of a telomere sequence and late chromosome 17q gainGudrun Schleiermacher
, , Institut Curie, 26 rue d'Ulm, 75248 Paris Cedex 05, France
Oncogene 24:3377-84. 2005..Finally, screening of a panel of neuroblastoma cell lines identified interstitial telomeric sequences in three other cases, suggesting that this may be a recurrent mechanism leading to unbalanced translocations in neuroblastoma...
