N PakkasjärviSummaryAffiliation: University of Helsinki Country: Finland Publications
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Detail Information
Publications
Unraveling the disease pathogenesis behind lethal hydrolethalus syndrome revealed multiple changes in molecular and cellular levelHeli Honkala
National Institute for Health and Welfare and FIMM, Institute for Molecular Medicine Finland, Helsinki, Finland
Pathogenetics 2:2. 2009..HLS is caused by a substitution of aspartic acid by glycine in the HYLS1 protein, whose function was previously unknown...
Lethal congenital contracture syndrome (LCCS) and other lethal arthrogryposes in Finland--an epidemiological studyNiklas Pakkasjärvi
Department of Molecular Medicine, National Public Health Institute, Biomedicum, Helsinki, Finland
Am J Med Genet A 140:1834-9. 2006..LCCS is noted as a unique Finnish disorder with a prevalence of 1 in 25,250 (0.40/10,000) births and is a major cause of lethal arthrogryposis in Finland...
Respiratory distress secondary to nasopharyngeal glial heterotopiaN Pakkasjärvi
Department of Pediatric Surgery, Hospital for Children and Adolescents, University of Helsinki, Helsinki, Finland
Eur J Pediatr Surg 18:117-8. 2008..A high degree of suspicion, early diagnosis and surgical management are essential to cure this rare and potentially life-threatening disorder...
