Research Topics
Species | Paul A JamesSummaryAffiliation: Genetic Health Services Victoria Country: Australia Publications
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Detail Information
Publications
Breast cancer risk is not increased in individuals with TWIST1 mutation confirmed Saethre-Chotzen syndrome: an Australian multicenter studyPaul A James
Genetic Health Services Victoria, Murdoch Children s Research Institute, Melbourne, Australia
Genes Chromosomes Cancer 48:533-8. 2009..These results provide clinical reassurance that at present there is no evidence for breast cancer screening above standard practice for individuals with SCS...
High-level 46XX/46XY chimerism without clinical effect in a healthy multiparous femalePaul A James
Genetic Health Services Victoria, Murdoch Children s Research Institute, Melbourne, Victoria, Australia
Am J Med Genet A 155:2484-8. 2011....
Extending the scope of diagnostic chromosome analysis: detection of single gene defects using high-resolution SNP microarraysDamien L Bruno
VCGS Cytogenetics Laboratory, Murdoch Children s Research Institute, Royal Children s Hospital, Parkville, Australia
Hum Mutat 32:1500-6. 2011..The importance of astute clinical assessment and laboratory-clinician consultation is emphasized to optimize the value of microarrays in the diagnosis of disorders caused by single gene copy number and sequence mutations...
Optimal selection of individuals for BRCA mutation testing: a comparison of available methodsPaul A James
Familial Cancer Centre, Murdoch Children s Research Institute, Melbourne, Australia
J Clin Oncol 24:707-15. 2006..We examined the performance of six different methods with the aim of identifying an optimal strategy for selecting individuals for mutation testing in clinical practice...
Phenotypic variability of distal 22q11.2 copy number abnormalitiesTiong Yang Tan
Genetic Health Services Victoria, Melbourne, Australia
Am J Med Genet A 155:1623-33. 2011..Patients with distal chromosome 22q11.2 copy number abnormalities exhibit inter- and intra-familial phenotypic variability, and challenge our ability to draw meaningful genotype-phenotype correlations...
